Ezempilo, Izifo Nezimo
Isifo sikaLou Gehrig: izimbangela, izimpawu kanye nokwelapha
Isifo sikaLou Gehrig noma i-amyotrophic lateral sclerosis yisifo esingavamile, kodwa esiyingozi kakhulu. Lesi sifo sihambisana nokubhujiswa kancane kancane kwe-motor neurons, okuyinto, ngokufanele, ithinta umsebenzi wezicubu zomzimba. Ngeshwa, namuhla akukho mithi engayiphulukisa lesi sifo. Imithi yanamuhla inganikeza kuphela izindlela ezisiza ukuyeka izimpawu eziyinhloko.
I-Lou Gehrig syndrome kanye nezimbangela zayo
Kuze kube manje, izimbangela zalesi sifo aziziwa. Yiqiniso, izikhungo eziningi zokucwaninga aziyeki ngokuzikhandla izici ezingabangela ukubola kwesibalo, kanye nezindlela zokwelashwa okuphumelelayo.
Noma kunjalo, ososayensi bakwazi ukuthola ezinye zezici ezingozi. Ngokuyinhloko, lesi sifo sivame ukutholakala kubantu abathintekayo emzimbeni wabo, ikakhulukazi insimbi enamandla kakhulu, isikhathi eside. Kulezi zici ezingozini zingabalwa futhi zilimale eziningi. Kuphela ku-3-7% kweziguli ezitholakale zinefomu elingavamile le-multiple sclerosis.
Ngendlela, lesi sifo sathola elinye lamagama alo ngokuhlonipha uLou Gehrig. Lo ngumdlali odumile wase-American baseball, owawuneminyaka eminingi ekwazi ukulwa nalesi sifo.
Isifo sikaLou Gehrig nezimpawu zayo
Masinyane kufanele kuqaphele ukuthi izibonakaliso zokuqala ze-sclerosis zivele zivele zikhulile noma zigugile. Njengoba sekushiwo kakade, lesi sifo sihlotshaniswa nokubhujiswa kwama- neurons. Ngenxa yokungabi nalutho, imisipha ilahlekelwa ikhono lokuthola inkontileka. Njengomthetho, izicubu ze-muscular of the end are primarily affected. Lesi sifo siqhubeka sithuthuka, sichitha izintambo ezinomsolo ezisele.
Ubuthakathaka kancane kancane i-atrophy, ngenxa yesiguli esilahlekelwa ikhono lokuhamba. Njengomthetho, abantu abagulayo ngeke basakwazi ukunakekela ngokwabo - ngokuhamba kwesikhathi kunzima nabo ukuba bagcine isiqu sabo endaweni eqondile.
Ngeshwa, i-sclerosis ayipheli lapho. Lesi sifo sikaLou Gehrig asiphazamisi nje imisipha yamathambo. Ekuqaleni, i-pharynx ihlupheka, ngenxa yokuthi isiguli asikwazi ukugwinya ngokuzimela. Njengoba ukuqhubekela phambili kuqhubeka, inqubo ye-sclerotic ihlanganisa imisipha ye-intercostal kanye ne-diaphragm. Ngakho-ke, umuntu ulahlekelwa ikhono lokwenza ukunyakaza kokuphefumula. Kule nkinga yesifo, ukugcina imisebenzi ebalulekile, kuyadingeka ukusebenzisa i-apparatus for ventilation yokufakelwa.
Isifo sikaLou Gehrig asithinti ukusebenza kwezitho zomqondo. Umuntu angabona, azwe, adle futhi anuke futhi aqonde ulwazi ngokwanele. Kuphela kwezinye izimo, ukuphazamiseka kwengqondo kungenzeka .
Isifo sikaLou Gehrig nezindlela zokwelapha
Njengoba sekushiwo kakade, akunakwenzeka ukuphilisa lesi sifo namuhla. Imithi inganikeza ukunakekelwa kwekhwalithi kuphela, uhlelo lokuvuselela kanye nokwelashwa okuyisimangaliso. Kuze kube manje, isidakamizwa esithi "i-Riluzol" yisidakamizwa esisodwa noma esingaphansi komuthi okuvumela ukuthi ukwandise impilo yesiguli izinyanga eziningana noma iminyaka.
Ngaphezu kwalokho, ukuhlinzekwa kwezidakamizwa kusetshenziselwa ukuthuthukisa isimo sesiguli. Ngaphambi kokucindezeleka noma ukuhlaselwa kwesibindi, kusetshenziselwa izidakamizwa kanye nezidakamizwa zokucindezeleka. Ukuzivocavoca umzimba njalo okuthiwa "ukwelapha emsebenzini" kunciphisa inqubo ye-muscle atrophy.
Isibikezelo kubantu abane-syndrome enjalo, ngeshwa, asibi. Ezimweni eziningi, isiguli sigcina ukuhlala esinye iminyaka engu-2-6 ngemva kokubonakala kwezimpawu zokuqala. Kuphela kwamaphesenti angu-10 kuphela okulindeleke ukuthi kube khona isikhathi sokuphila kweziguli ezingaphezu kweminyaka eyishumi.
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