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Frederick syndrome: ukwelashwa kanye nokuvimbela

Frederick syndrome ngokuthi ngempela ukungasebenzi ezibucayi inhliziyo, okokuqala kwatholakala ukuthi nginesifo physiologist ezivela eBelgium Leon Frederick ngo-1904. Nakuba lesi sifo ngizwile ambalwa, kwenzeka kaningi.

Ngasekuqaleni ekwelapheni lo mkhuba Frederick ngenkuthalo wayekwenza ukusetshenziswa ejenti anticholinergic, kodwa ngoba kungabangela nokugula ngengqondo, ezokwelapha zesimanje ezihamba kude nawo.

incazelo syndrome

Frederick Syndrome luyinhlanganisela nezimpawu isici umnyuziki transverse ukuvinjelwa kanye fibrillation atrial.

Ngesikhathi esifanayo enqabe yezinzwa ayeke ngokuphelele iyangena ventricles kusukela Atria, okuyinto balahlekelwe ikhono njalo nokwehla ehlelekile.

Ukungabikho pulses okuthakazelisayo kubangela ukwakheka ezindongeni noma phansi atrioventricular engeyokuqala foci ventricles kuthiwa ngokwabo ukuqala ukukhiqiza yezinzwa. Kuba uhlobo isinxephezelo, kodwa asisho londoloza isimo, ngoba ukuntuleka ishayela imvamisa (okungenani amashumi amane anamanci mathandathu isignali).

Ngenxa yalokho, i-ventricles wenhliziyo ungenwa kancane kunalokho umuntu enempilo, futhi ngaleyo ndlela kubambezela negazi ukugijima, okubangela anoxia futhi kunengozi enkulu nesifo esibizwa ngokuthi i- "syndrome ka uFrederick."

Izimpawu main

Phakathi izimpawu eziyinhloko yalesi sifo (noma mkhuba) Frederick ihlaba umkhosi:

  • Smooth, kodwa kancane ishayela.
  • Isiyezi.
  • Ubuthakathaka.
  • Ukuphelelwa ngumoya.
  • Ukukhathala.
  • Ukozela.
  • Ekuqulekeni.

Konke lokhu kungenxa ejwayelekile isimo lapho ubuchopho ongawamukeli-mpilo ngokwanele.

Izimbangela sifo

Frederick syndrome ingekho a cleaner, uma inhliziyo enempilo. It is phetho emibi umphumela izifo ezifana:

  • isilethikusebenza.
  • Inhliziyo yayo yayinezinkinga ezicini.
  • isilethikusebenza.
  • Myocarditis.
  • Zenhliziyo.
  • Angina.

Lezi zifo kubangele izinqubo sclerotic bemvelo, lapho inhliziyo ikhula ezicutshini. nokumiselelwa Kugcine futhi uthatha indawo yabo amaseli, okuyinto nje inomthwalo wokukhiqiza futhi ukudluliswa kwe-amaza kagesi.

Sifo Frederick mkhuba

Ngenxa izimpawu zalesi sifo zifana izimpawu ezinye izifo eziningi, ukuxilonga syndrome ka Frederick kungenzeka kuphela ngosizo indlela ye electrocardiogram.

Futhi ukubukela ukuziphatha inhliziyo kuyinto efiselekayo usuku ukuze ubone ukuthi kuyinto isigqi ngezikhathi ezahlukahlukene imini nobusuku, ukuze ubone ukuthi ophendulayo imisipha yenhliziyo kuya umthwalo, nokunye.

Ngokuvamile uphethwe "Frederick syndrome" ECG kanje:

  • Amazinyo R angekho, bona esikhundleni siyafiliza noma likhona wave uhlamvu (f futhi F).
  • ventricular izinga avamile, kodwa isibalo amabhithi ngeminithi akuyona izikhathi ezingaphezu kuka-40-60.
  • Ngo ukwakheka isigqi engxenyeni engezansi atrioventricular uxhumano Ventricular izakhiwo mincane futhi abe evamile, ngaphandle ukuphambuka, morphology.
  • Uma kwakhiwa isigqi is e ezindongeni izakhiwo ventricular zibukeka enwetshiwe zikhubazekile.

Frederick syndrome: ukwelashwa kanye nokuvimbela

Ekukhombeni izimpawu ezichazwe ngenhla, qiniseka ukuthi ubona udokotela wakho futhi uhlolwe. Anoxia - isimo esiyingozi kungabangela kwezinso sina ebuchosheni. Futhi lapho Frederick syndrome ke kungathatha imizuzwana emihlanu eziyisikhombisa lapho inhliziyo ngempela eyeka (kwenzeka ezimweni lapho kungekho isinxephezelo ishayela ngesimo ventricular isigqi).

Imiphumela yaloku kuhlola okungenhla Esifike Ngesikhathi luzoncipha izingozi, kanye nokwelashwa uyombhubhisa sifo siphile ukuphila okwanelisayo. Izibikezelo Evumayo lesi sifo.

Kuze kube manje, uFrederick syndrome iqhubeka, njengoba umthetho, indlela ukugxilisa i nolwelwesi ku imisipha yenhliziyo, oveza lo pulses esikhundleni sohlelo Atria. I electrode efakwe ventricle, futhi isigqi yayo kuyinqubo ehlelwe kusengaphambili futhi incike yobudala kanye isimo jikelele isiguli.

Prevention njengoba enjalo ayikho. Kuyinto ukuvimbela kanye nokwelashwa lesifanele izifo ezibangela lesi simo.

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