Impilo, Izifo nemibandela
ALS (isifo): Izimpawu nezindlela uphethwe
Isimiso sezinzwa somzimba womuntu usengozini kakhulu. Yingakho kukhona izifo eziningi ezahlukene ezingathinta le ngxenye ethile yomzimba. Kulesi sihloko ngifuna ukukhuluma ngalokho-ALS (isifo). Izimpawu, imbangela isifo, kanye nezindlela ukuxilongwa kanye nokwelashwa kungenzeka.
Kuyini lokhu?
Ekuqaleni, kudingeka uqonde nemiqondo eyisisekelo. Kubalulekile futhi kakhulu ukuqonda ukuthi BAS (isifo), izimpawu zesifo kuzoxoxwa ngemva kwesikhashana. Incazelo izifinyezo: atrophic lateral sclerosis. Lapho lesi sifo sihlasela izinzwa lomuntu, okungukuthi ahlupheke Izinzwa. Basuke etholakala cortex cerebral futhi izimpondo anterior ka emgogodleni. Kubalulekile ukusho ukuthi lesi sifo esingelapheki, ngenhlanhla sesiyazi, okwamanje alelapheki.
izinhlobo
Kukhona futhi izinhlobo ezintathu zesifo ezifana ze-ALS:
- zakudala okungatheni. It is hhayi ngofuzo. Lokho-ke seyihlanganisa 95% azo zonke izifo.
- Ukubambezeleka (noma umndeni). Njengoba siye saba sobala, it is ngofuzo. Nokho, kule uhlobo lwesifo libhekene ngokubonakaliswa kamuva izimpawu.
- Guam-uhlobo noma ukuma Mariana. sici laso eliyingqayizivele kubonakala phambi ezimbili ngenhla. ukuthuthukiswa Slow lesi sifo.
Izimpawu zokuqala
Kuwufanele ethi izimpawu zokuqala zesifo ingelashwa futhi isiphi esinye isifo. Yilokho inkinga inkohliso; ukuxilonga ngokushesha cishe akunakwenzeka. Ngakho, izimpawu zokuqala ze-ALS zimi kanje:
- Ubuthakathaka bemisipha. Ngokuyinhloko kuziwa emaqakaleni futhi izinyawo.
- Yoma izandla, ubuthakathaka imisipha. Iphinde singenzeka dysmotility.
- Iziguli kusaqalwa lesi sifo kungase kancane droop stop.
- Libhekene gqwa kwemisipha izinhlungu zibe. Can ukudikiza emahlombe akhe, izandla, nolimi.
- Nemilenze buthaka. Isiguli kanzima angahamba amabanga amade.
- Libuye isici ukubukeka dysarthria, isb inkulumo sifo.
- kuqala nobunzima ukugwinya kwenzeke.
Uma isiguli sine-ALS (isifo), izimpawu ukuthuthukiswa sifo ozokhula, sikhule. Okulandelayo, isiguli singase ngezinye izikhathi singazizwa kumnandi oludlulele noma ukudabuka. Yoma singenzeka ulimi futhi disequilibrium. Konke lokhu kungenxa yokuthi lowo muntu iyahlupheka umsebenzi ephakeme engqondo. Kwezinye izimo, ngaphambi kukhona izimpawu ezinkulu zingaphazamisa umsebenzi engqondweni yethu. okungukuthi komqondo livela (lokhu kwenzeka njalo, cishe 1-2% of amacala).
ukuqhubekela phambili kwesifo
Yini enye kubalulekile ukwazi abantu abanesithakazelo kuyi-ALS edluliselwa (isifo)? Izimpawu ezenzeka isiguli njengoba isifo kungathiwani lokho ncamashi uhlobo yakhe yesifo:
- ilungu ALS. Umlenze wokuqala senzeka ukuhlulwa. Ngaphezu kwalokho iqhubeka ukwephulwa kwemilenze noma.
- Bulbar ALS. Kulokhu, izimpawu ezisemqoka ukwephulwa inkulumo umsebenzi, kanye nezinkinga nge ukugwinya. Kuwufanele ethi lolu hlobo sifo ingasaphathwa ezivamile kulokuqala.
ukwanda izimpawu
Yini okufanele ukwazi isiguli unesifo like i-ALS? Izimpawu yenu kuyovumelana kancane kancane ukwandisa, esitho ukusebenza kuzoncishiswa.
- Kancane kancane lapho sokugembula Babinski, lapho kuthinteka kukhona engenhla Izinzwa.
- imisipha ithoni, ikhaliphe buyothuthuka ukuba ngcono.
- Kancane kancane bayomangala futhi aphansi Izinzwa. Kulokhu, isiguli uyozizwa jerking okungalindelekile yezingalo nemilenze.
- Kulesi kuhle ngokuvamile in iziguli womuntu okucindezeleka, kukhona melancholy. Zonke ngoba Umuntu ulahlekelwa ikhono ukusinda ngaphandle kosizo, awubange usayithola ikghono.
- ALS izimpawu futhi ezihlobene umgudu wokuphefumula: isiguli siqala ukuphefumula ukuphazamiseka.
- Futhi, akunakwenzeka ukuba self-catering. Isiguli ngokuvamile ifakwe ngamapayipi lapho indoda futhi ithola yonke kunesidingo sokuba khona ukudla.
Kuwufanele ethi ALS kuhle kungenzeka ngokushesha. Izimpawu esemncane ngeke sihluke izimpawu isiguli, izimpawu zabo uqala ukuvela ngemva kwesikhathi eside kakhulu. Konke kuncike umzimba, kanye uhlobo lwesifo. With ukuthuthukiswa sifo kancane kancane ukukhubaza Umuntu ulahlekelwa sinekhono abaphilayo ozimele. Ngokuhamba kwesikhathi, inqatshelwe ngokuphelele esitho.
Isigaba sokugcina
Ezigabeni lokugcina isifo isiguli ngokuvamile kuba kahle umsebenzi zokuphefumula, ukwehluleka okungenzeka bakwenza kwemisipha yokuphefumula. Ezimweni ezinjalo, iziguli kudingeka ukupholisa. Ngokuhamba kwesikhathi, ungakwazi ukuthuthukisa umsebenzi amanzi emzimbeni, okuvame ukuholela yokuthi ijoyina igciwane yesibili, elibuye obulala nesineke.
ukuhlola
Njengoba isifo efana ALS, izimpawu, uphethwe - yilokho engifuna ukukutshela futhi. Kuwufanele ethi lesi sifo sitholakala avame a inqubo ukuqedwa nezinye izinkinga emzimbeni. Uma isiguli esilandelayo izindlela zokuxilonga ingase yabelwe:
- Igazi test.
- Imisipha biopsy.
- -X-ray.
- Ukuhlolwa ukunquma ukunyakaza kwemisipha.
- CT, i-MRI.
kwamangqamuzana
Kuwufanele ethi lesi sifo inezimpawu ezenzeka kanye nezinye izifo. Ngakho-ke kudingekile ukuba ukuhlukanisa ALS nezinkinga ezilandelayo:
- myelopathy wesibeletho.
- Ukudakwa ngu mercury, okuhola manganese.
- Syndrome izimpisi ibha.
- Malabsorption syndrome.
- Endocrinopathy et al.
ukwelashwa
Bit kubhekwe isifo efana ALS, izimpawu, ukwelashwa - yilokhu futhi kudingeka sinake ekhethekile. Njengoba sekushiwo ngenhla, ngeke welaphe ngokuphelele. Nokho, kukhona izidakamizwa ezisiza ukubambezela inkambo isifo. Kulokhu, iziguli kaningi ukuthatha imithi efana "Riluzole", "Rilutek" (nsuku zonke kabili ngosuku). Kuyinto ukwazi ukuvimbela kwezulu kancane glutamine, ikhemikhali kuthinta Izinzwa. Nokho, liphinde ewusizo izindlela ezihlukahlukene zokwelapha, umgomo wakhe oyinhloko - ekulweni izimpawu eziyinhloko:
- Uma isiguli ecindezelekile, lapho antidepressant, zinhlungu ezingahle zinqunywe wumgomo.
- Lapho imisipha spasm kubalulekile ukuthatha imisipha relaxants.
- Uma kudingeka, izinzwa angabelwa, lapho besanda ngasekupheleni zesifo - opiates.
- Uma isiguli uye siyabhubha ubuthongo, kudingeka benzodiazepine izidakamizwa.
- Uma kukhona inkinga webhaktheriya kudingeka imithi elwa namagciwane eyanele (nge bass ngokuvamile kuphakama izifo bronchopulmonary).
Izinsiza:
- kokwelashwa.
- Slyunootosos noma ethola izidakamizwa ezifana "Amitriptyline".
- Tube yokudla, ekudleni.
- Ukusetshenziswa kumadivayisi ahlukahlukene ukuthi anganikeza ukunyakaza nesineke: imibhede, izihlalo, izinti ukuhamba, ezinjengenyanga ekhethekile.
- Kungase kudingeke ukupholisa lokukhanda.
Imithi yendabuko, ukutshopa lesi sifo kukhona alunamsebenzi. Kufanele wathi akuyona nje kogulayo kuphela kodwa umndeni wakhe ngokuvamile udinga usizo owelapha.
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