Impilo, Izifo nemibandela
Chorea - a ... Chorea ezinganeni. chorea rheumatism
Chorea - a zokugula isimiso sezinzwa. Libhekisela izinhlobo hyperkinetic. Lesi sifo kuhambisana izinkinga cerebral ISIZINDA subcortical. Kungaba ukukhomba izici isici: i episodic, zavela, ukudikiza esingalawuleki ezandleni nasezinyaweni, ngezinye izikhathi ebhuthini. Ezigabeni kamuva kukhona abakhubazeke ngokwenqondo nakongqondongqondo, izinkinga nekubambisana, futhi self-service. Ngokuvamile izingane chorea kuyinto iphutha ngomsebenzi evamile anda. Eqinisweni, lapho izimpawu zokuqala isifo kudingeke ufune usizo kumuntu ofanelekayo.
Igama elithi "chorea"
Igama elithi isetshenziswa ezimweni ezimbili. Lingase lisho isifo ezimele, okungokwendlela leli qembu (isib chorea encane Huntington noma chorea). Futhi isetshenziswa ukuchaza syndromes ezithile ezenzeka lapho izinhlobo ezahlukene izifo. Igama elithi "chorea" livela isiGreki, lapho kuboniswa uhlobo oluthile umdanso. Lokhu kuchaza izimpawu zokuqala, okuyinto azibonakalisa umkhuphuka, uncoordinated, nomqwayiba, ukunyakaza okusheshayo isiqu kanye emikhawulweni. Ukuziphatha isiguli ngempela okungalindelekile, umdanso kunezinxushunxushu. Kwasukasukela ngokuthi chorea "umdanso St Vitus sika." Leli gama lihlobene nezinkolelo St Vitus, okuyinto ngenkuthalo ubuKristu, ngoba ngalo wahlukunyezwa amasosha aseRoma yasendulo. Ngemva kokufa kwakhe waba legend ethandwa ukuthi uma othize ukwenza umdanso eziqhumayo emhlabeni ithuna lakhe ngosuku lwakhe lokuzalwa, uzophila ngecala lokuvukela vivacity namandla ka unyaka wonke.
izizathu
Izimbangela zesifo ingase ibe zasezindaweni ezihlukahlukene, kodwa ikakhulu chorea kubangele yokuba izici zofuzo eziyingozi noma izifo ezibangelwa ufuzo.
chorea Ngaphansi ezivamile, kubangelwa imvelo ezifana ezithathelwanayo izifo ezifana TB meningitis, encephalitis viral, neurosyphilis, isifo saseLyme, ukukhwehlela whooping. Elivela kuzo chorea lingaphathelaniswa ne ukungakhuli umzimba (uma kukhona isifo Fabry sika, Hyperglycemia, i-hyperthyroidism, noma isifo Wilson), intoxications (ushevu ngomlomo izinto zokuvimbela inzalo, mercury lithium, digoxin, neuroleptics, levodopa), pathologies sokuhlasela kwamasosha omzimba (ezifana antiphospholipid syndrome , omzimba izicubu erythematosus, yi-multiple sclerosis). Esinye sezizathu ukuthi kuvusa nesenzakalo lesi sifo, odokotela nabo ngokuthi ukulimala izakhiwo ingqondo. Lezi zihlanganisa isimila ekwakhekeni, hypoxic encephalopathy, ukulimala kuhlasimulise ubuchopho, imivimbo.
izimpawu ezivamile
Chorea - isifo kuzibonakalisa okungahleliwe, senhlekelele, yesikhathi esifushane komzimba ukunyakaza. Kwezinye izimo, le ukunyakaza zingafundwa njengoba evamile, eyanele, ejwayelekile Umuntu ophilile udinga, into ukukhathazeka. Kwezinye, ziyafana ngokomzwelo, umdanso ongalawuleki. Jerky Twitch kungaba ngomhlangano noma amabili emaceleni, kodwa abanayo okungenani ezinye uhlobo Synchronicity.
Kuye nalokho okutholakala ifomu zokugula, ukuhlukanisa izimpawu of chorea. Uma umuntu kancane liphinyiselwe hyperkinesis trochaic ke ukuziphatha kwakhe waphawula motor ukukhathazeka ezincane, ephelezelwa motor disinhibition, kukhuphuke emotionality, by ukuziphathisa ezithile, ukuyobayobeka, ukuthinta okungalungile.
amafomu Izindlala ibonakaliswe njengeyenziwe chorea ukunyakaza eyinqaba "yo yo". ifomu okunzima hyperkinesis trochaic obuhlanekezela ukunyakaza nokuhamba, inkulumo nesimo sobuso. Gait lesiguli akuyona kuphela ongaziwa, kodwa futhi ngesilinganiso esithile "clown". Chorea, izimpawu zazo okunzima kakhulu, ayivumeli ngisho okwenza eminye ukunyakaza. Iziguli isifo ezinzima axhomeke imvelo yabo, njengoba akusho ukuhambisa futhi kungaba ukuhlinzekela wena empilweni ngokugcwele.
chorea Huntington sika
Lokhu zokugula kuzibonakalisa ezimweni eziningi abaneminyaka ephakathi kwengu-35 kuya ku-45. Chorea, izimpawu zazo, ngaphezu hyperkinetic ejwayelekile, baphathe iziyaluyalu ubuntu kakhudlwana futhi komqondo (ukwehla intelligence) eba kancane kancane, ngezinye izikhathi kwakuba nzima ukulandelela okwamanje lapho baqala ukuvela. Ukunyakaza lokuqala enobudlova ngokuvamile kwenzeka ebusweni. Abakwazi kudidaniswe okungahleliwe motor automatisms (lolu limi ophumile, obuswacile, ikhotha izindebe, umlomo). Ukuqhubeka kwesifo kubonakala ukuthuthukiswa hyperkinetic ebhuthini futhi emikhawulweni. ifomu Sinzima libhekene abanokukhubazeka yokukhuluma, inkumbulo, inqubo nokugwinya, lizinga self-service bese iphela komqondo. Qala i- chorea Huntington sika kukhona okuthile engqondweni ngesimo iziyaluyalu hallucinatory-Paranoid, ngokomzwelo futhi kokuziphatha.
Neyroakantotsitoz
iziguli Neyroakantotsitozom ahlupheke hyperkinesis hhayi kuphela trochaic, kodwa acanthocytosis (izinguquko yakha amangqamuzana abomvu egazi). Ukuhlukanisa sici kule zokugula kuyinto yoma (ubuthaka imisipha emikhawulweni engenhla nengezansi). Phakathi kwezinye izici ukuhlukanisa izifo: hyperkinesis ngomlomo ukuhlafuna ukunyakaza, jerking lip aphumele ulimi kanye nezinye ubuso. Lapho neyroakantotsitoze nesineke yezimo abhekene iskusyvaet nolimi lwakhe, izindebe nezihlathi ebusweni engaphakathi igazi. Isici nzima kule isifo kanye komqondo aphume ashone nokuquleka.
Izifo Lesch-Nai Han
izifo azalwa naso isimiso sezinzwa ukugxambukela ukuba umuntu aphile ukuphila okwanelisayo. Lezi pathologies isifo esihlobene futhi Lesch-Nai Han. Imbangela eyinhloko sifo nokuntuleka lezinceku hypoxanthine-guanine. Lokhu chorea ezinganeni kuhambisana thuthuva sina ekusebenzeni isimiso sezinzwa. Futhi zokugula sokucasuka ukukhiqizwa lelitfutfukile uric acid.
Kusukela ezinyangeni zokuqala zokuphila ingane oboné ukubambezeleka ukuthuthukiswa. Rigidity yezingalo nemilenze kuboniswa ngenyanga yesithathu. Kusukela ngonyaka wokuphila wesibili ingane kokuba grimaces ezithile ebusweni, okuthi ahambisana izimpawu pyramidal ipheshana izilonda futhi imisiwe kwengqondo. Baby kungaba ngokomzimba ukulimaza, nxa bezilinganisa ngezingqobo iluma izindebe zabo noma iminwe.
chorea ingozi
Chorea Benign ezinganeni kuzibonakalisa ebeleni noma ingane isencane. Pathology libhekisela izifo sitholwa njengefa. hyperkinesia generalized kule isifo ezikhoselweni kuphela uma ingane ilele. Kusukela chorea Huntington sika, lolu hlobo zokugula ihlukile non-progressors nokuthuthukiswa evamile intelligence. Ngo yobudala amadala chorea ingozi Ungakwazi ukunciphisa hyperkinetic, uma isikhathi ukuxhumana isikhungo sokwelapha.
amafomu yesibili chorea
ezivamile Amafomu yesibili isifo ezibhekwa ezimbili: chorea futhi chorea yokukhulelwa.
Eyokuqala libizwa chorea Sydenham sika. ukubukeka kwakhe kungase kumkhathaze acute ukutheleleka streptococcal noma imfiva rheumatism. ifomu Ezintsha libhekene umhlibitho nehaba, ukuthinta bayaxoxa, ukunyakaza disinhibition. Izindlela eziyinkimbinkimbi hyperkinesis trochaic ebonakaliswa yokuthi isiguli kunzima ukuhambisa, nokukhuluma kahle, ngisho ukuphefumula. Lapho lesi sifo kwenzeka ngokuthi "tonic" emadolweni futhi elisheshayo "iyelapheka", iziyaluyalu ngokomzwelo futhi ngokomzwelo, umfutho ophakeme wegazi kwemisipha.
chorea abakhulelwe - isifo elisuka ebuntwaneni. Lokho, ezonini engozini yilawo besifazane abaye ihlangabezane ingane nge choir encane. Pathology singenzeka ngesikhathi sokukhulelwa lokuqala izinyanga 2-5. Ngokuhamba alandelayo isimo "ezithakazelisayo" ingase futhi kuphakama chorea. Ukwelashwa ezimweni ezinjalo ezingajwayelekile, njengoba isifo ubalekela ngokwalo ngemva kokuphazamiseka bekhulelwe noma ngemuva kokubeletha.
chorea rheumatica
Indawo okuvela kuyo amazwi isifo iza kwezinhlansi kuqiniswa imfiva rheumatism noma endocarditis, okuyinto kuhambisana valvular isifo senhliziyo. Ezimweni eziningi zesifo akuzona ahlobene kule isici, futhi lesi sifo kubonakala ngokuzimela.
chorea Rheumatic avame esizithinta ngayo izingane ezineminyaka ephakathi kuka-iminyaka 6 no-15. Ngo amantombazane, lo zokugula landile. Ngo esigabeni sokuqala lesi sifo kungaba isizathu sokukhathazeka, ngoba izimpawu anqunyelwe grimaces, kanye nabazali uthatha njengelungelo ihlaya. Inqubo ukunyakaza okungalindelekile elincane nasemilenzeni, uthome tintwane kancane kancane zisakazeka kuwo wonke umzimba. Ngemva kwesonto kufika isikhathi ukuboniswa, lapho ukunyakaza kwengane kuyashesha futhi siye phambili. Lesi simo kuvikela ingane ukuqhubeka nokusebenza evamile, okungukuthi, ukuba adle, ukuhamba, ukubhala.
chorea Rheumatic obuhlanekezela ubuso bomntwana nezinkulungwane grimaces. amafomu Sinzima lesi sifo liphazamisane nesineke asukume, ukugwinya, ukukhuluma, futhi umzimba butjhilweni. Uma kutholakale ukuthi une-chorea, ukwelashwa kufanele kwenziwe kahle futhi ngokushesha.
ukuhlola
chorea okusolwayo kuphakama ngenxa kuyinqaba. Encwadini Nokuhlola kokuqala, udokotela kufanele ubambe ingxoxo isiguli noma umndeni wakhe. Ikakhulukazi kubalulekile ukwazi ukuthi othile ogulayo umuntu emndenini yalesi sifo, esingakanani babe nezimpawu chorea, kungakhathaliseki isiguli wathatha izidakamizwa, kungakhathaliseki izifo ukuvuvukala wahlupheka. Uchwepheshe Ngaphezu kwalokho kumele ihlole ukunyakaza okungalindelekile. Kuyadingeka lokwenza ukuxilongwa kanye nencazelo izifo ezingaba kuhambisane chorea, kubangele sina ukuphambuka bokusungula. Izimpawu lezi zifo ungalilahli njalo manifest. Ngezinye izikhathi, ukuze sithole kahle kwezinso ezifana ngendlela efanele usaqala, isakhiwo Kwenziwa survey. Ukuhlolwa kwegazi sizobonisa ezingeni ithusi igazi khona noma ukungabi khona izimpawu ukusabela ukuvuvukala. Ngaphezu kwalokho, afeze ikhompyutha tomography,-magnetic resonance imaging, electroencephalography.
ukwelashwa
Chorea - a zokugula ukuthi akuvumeli nesineke ukuqhuba evamile impilo egcwele, ngakho kufanele aphathwe ngendlela okufika ngesikhathi futhi ephelele. Amaqhinga ukwelashwa incike izizathu adala izifo. Ngokwesibonelo, ngo-nesineke isifo Wilson ezinqunyiwe ukudla nge okuqukethwe ubuncane zethusi izidakamizwa kabani isinyathelo sibhekiswe ekunciphiseni ukumuncwa yayo.
Chorea Huntington ebekiwe neuroleptics futhi benzodiazepine zinhlungu. Uma chorea kubangelwa esingamahlalakhona njalo cerebral ukugeleza kwegazi, kukhona isidingo izidakamizwa ukuthi kunciphise umfutho wegazi. Vasculitis eyenziwa ukwelashwa kwama-hormone. Uma avele izimpawu generalized kakhulu, ukwelashwa kufanele kube eziyinkimbinkimbi.
Nciphisa ukushuba ukunyakaza okungalindelekile kungenzeka esebenzisa kokungenela kuhlinzwa, lapho ukubhubhisa nucleus ventrolateral we thalamus. Chorea udinga ukuthatha imithi ukuthi ngcono ukusebenza kwengqondo kanye nokudla, kanye namavithamini yeqembu B.
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