Impilo, Imithi
Banti sika Syndrome: Izimpawu, Ukwelashwa
"Syndrome" ngesiGreki lisho "cluster" noma "kwakwakhe". Kwezokwelapha, le ncazelo inikezwa izifo ukuthi abe inani elithile izici liyabonakala, ngokuvamile bavele ndawonye. Ngakho, inhlanganisela yezici ukusazi ngokunembile isifo esikuphethe kungenziwa ngokuthi a syndrome. Enye yalezi uthi - Banti Syndrome.
sici
Hepato-splenic syndrome - ke igama lesibili lesimo. It libhekene kweNdikimba isibindi ubende, ngokulandelana, kwaphazamisa lezi zitho. Banti Syndrome okwenzeka ngenxa yezifo ezingalapheki kohlelo hepatobiliary , futhi iziyaluyalu kwegazi "esangweni Vienna -. Vienna ubende"
Emithambo yegazi kwegazi isibindi ubende inikeza incazelo kanjani lezi zindikimba uxhumekile bese Indlela Ezisithinta nomunye ukuphambuka ezifana Banti syndrome. Ungakwazi ukulandelela uxhumano emithambo yegazi phakathi kwalezi zinhlangano.
Ikhaya Vienna - iyona portal. Ngo igazi yakhe eqoqwe kusukela ubende kanye nezinye izinhlaka ngaphakathi komgodi ongaphakathi kwamathumbu. Wabe iwela isibindi, lapho ohlanziwe ubuthi eziyingozi bese ibhebhetheka kulo lonke izakhi zomzimba. Ingxenye vein portal splenic, ubende ke uku-ubuhlobo obuseduze kakhulu isibindi izinqubo ezenzeka kuwo. Yilesi isizathu esenza ukuba, e Banti sika sifo sithinta sesibindi ubende.
Pathogenesis syndrome hepatolienal
igazi disorder kungaba ngenxa ukuvaleka mafutha anciphisa isikhala esingaphakathi we vein portal. Kukhona yokujama tsi wegazi futhi ngenxa yalokho, ukwandisa wegazi. Kungani lokhu kwakwenzeka? Nazi ezinye izizathu:
- kokucindezelwa Lwangaphandle vein portal. Lokhu kungenzeka kokubili ngaphakathi isibindi, futhi lenqwaba hepatoduodenal emnyango emzimbeni. Kulokhu, sebenzisa hepatolienal izimpawu syndrome kungenzeka nge izifo ezifana:
- Isifo sokusha.
- ifomu Sinzima zokusha kwesibindi.
- Thrombosis ka vein portal futhi imithambo eduze ezinkulu.
- kwezicubu isibindi isimila Primary.
- zokugula senhliziyo we senhlitiyo.
- Biliary izifo, izimila kanye izinhlumba.
- Hepatic vein thrombosis.
2. ukuvaleka mafutha anciphisa isikhala esingaphakathi we umthambo:
- Thrombosis ka vein portal amagatsha awo ezinkulu.
- Hepatic vein thrombosis, noma Budd-Chiari syndrome.
Ngaphezu izici elimazayo ezingase zibangele kweNdikimba isibindi ubende, lokhu kungase namanje ngenxa yokuphatheka ukuzivikela kuya ingress kwamagciwane.
esigabeni
Kunezigaba eziningana hepatolienal syndrome:
- Isigaba sokuqala singenzeka eminyakeni embalwa. Isimo jikelele eyanelisayo, kukhona omnene kwegazi, leukopenia futhi neutropenia. Isibindi ukhulise, kodwa kuba ubende okuningi.
- Isigaba sesibili libhekene nokwanda okuphawulekayo kwesibindi. Kukhona izimpawu ukusebenza yayo. Kungaba izinyanga eziningana.
- Isigaba sesithathu. ubude bayo - cishe elilodwa ngonyaka. Libhekene ngokunciphisa inani sesibindi uphawu kwandisa kwegazi, zikhona izimpawu nomfutho wegazi ophezulu, ascites, ukopha emathunjini, varices ngomphimbo.
- Isigaba sesine. cachexia Akumangalisi, ukuvuvukala, kanye ukopha izimpawu.
izimbangela
Ngokuvamile, Banti Syndrome ezinganeni.
Izimbangela kokubili ngabantwana nangabantu abadala zingase zishintshe:
- izifo Ukubambezeleka.
- Izifo ezithathelwanayo.
- Azalwa naso isifo sokulahlekelwa igazi hemolytic.
- yesifo azalwa naso futhi wathola ka vein portal, splenic.
- isifo Hemolytic ngayo lapho usana.
- ukuluthwa utshwala Okungalapheki.
amaqembu ingozi futhi ezisuka kusukela lezi zimpawu
Zonke izifo ukuthi kungabangela Banti Syndrome zingahlukaniswa ngamaqembu:
- Olunamandla futhi isifo sesibindi esingelapheki kubantu. Ukuze leli qembu libhekene ubuhlungu noma umuzwa wobukhulu ku hypochondrium kwesokudla, iziyaluyalu dyspeptic, pruritus, jaundice. Izizathu ingase ibe ku-hepatitis viral, xhumana neziguli ezithathelwanayo, kokungenela kuhlinzwa noma ukulimala, ukuba umlutha wotshwala, izidakamizwa reception gepatoksicheskih idluliselwe acute ubuhlungu besisu, imfiva.
- izifo Storage. Basuke waluthola emalungwini omkhaya owodwa noma eziseduze.
- Izifo ezithathelwanayo kanye yisinanakazana. Ehamba kahle kuchazwa ukudakwa, imfiva, arthralgia, futhi myalgia.
- Izifo uhlelo senhliziyo nemithambo yegazi. Basuke ephelezelwa tachycardia, ischemicheskoy isifo senhliziyo, i-ekuqongeleleni oketshezini ingaphakathi pericardial, ukwanda kanye ushintsho ukucushwa kwe-inhliziyo.
- Izifo wegazi nezicubu ze-lymph. Leli qembu libhekene izimpawu ezifana ukukhathala, imfiva, evuvukele zamanzi.
symptomatology
Uma ogulayo Banti Syndrome, izimpawu zingase zihlanganise:
- isibindi Ukwandiswa kanye ubende. Ubuhlungu ku palpation.
- Isisindo ukunciphisa.
- It kwaphazamisa nezindlala endocrine.
- Imiraro ipheshana wokugaya ukudla.
- Isifo sokulahlekelwa yigazi. Pallor kanye isikhumba esomile.
- ekuqongeleleni Okungenzeka uketshezi kule komgodi ongaphakathi kwamathumbu.
- Ubuhlungu bemisipha namalunga.
- Yellowing of ulwelwesi amaprotheni samehlo.
- Tachycardia, iphika.
- izinzipho ziyaqothuka, nezinwele.
Ukuze uphethwe kubalulekile ekuhlolweni, futhi kwaba isikhathi ukuhlaziya okuningiliziwe yemizimba - uphethwe.
ukuhlola
Uma uhlangabezana izimpawu ngenhla ukuxilongwa umehluko hepatomegaly futhi hepatolienal syndrome. Ukuze wenze lokhu, kudingeka sisebenzise ezahlukene imisebenzi. Elinye lamaphuzu wokuqala - ukuhlaziya jikelele igazi nocwaningo yayo kwamakhemikhali. Ukuze sithole isizathu esenza kwakukhona Banti Syndrome, uphethwe umehluko uyisidingo. Lalinama:
- Sonography kwesibindi kanye ubende, nenyongo sesinye, izitsha besisu.
- computed tomography.
- Iskena sesibindi ubende.
- -X-ray Ukuhlola duodenum.
- Laparoscopy.
- Punktsionalnaya biopsy kwesibindi kanye ubende.
- Ukuhlola umnkantsha futhi zamanzi.
Okwamanje isayensi hhayi emi namanje futhi sanda izindikimba sitholakele enjalo ukuhlaziya isimo njengoba Banti Syndrome. ukuxilongwa umehluko nalesi sifo umsuka isimo emitholampilo kwesibindi uma ikhona, kuba umsebenzi oyinhloko.
Ukwelashwa kanye nezinkinga lesi sifo
Njengomthetho, hepatolienal yokwelapha syndrome ukuhlonza eyisisekelo inqubo isifo kanye nokwelashwa kwayo. Ingane ayisona isifo ezimele. Uma uxilongwe "Banti Syndrome", ukuphathwa kufanele balondoloze gastroenterologist. Kulokhu, sebenzisa gepatoprotektory, antivirals, amahomoni namavithamini. Esimweni ngasinye, ukuba indlela ngamunye, ikhumbula etiology lesi sifo.
Uma singalitholi isifo futhi alikho ikhambi, onalesi sifo ungaba mubi kakhulu. Ngenxa yezinkinga yilesi sifo - a isifo sokusha kwesibindi, isibindi umthambo thrombosis, ukuvuvukala kwesinye inyongo izifo igazi. Ezimweni ezinjalo, ukususwa may izingxenye isibindi futhi ubende noma isitho ukufakelwa futhi igazi.
Ngo esigabeni sokuqala, Iziguli ziyakwazi ukuqhubeka asebenze futhi ekwazi ukumelana namandla umsebenzi kancane. Esikhathini esizayo, ne Ukuwohloka isimo isiguli ehlatshwa.
zokuvimbela
Ukuze ungalahlekelwa kuqale ukwakhiwa kwezinhlobo zokugula, kumele:
- ukuhlolwa ejwayelekile egazi noma omchamo.
- Isikhathi esijwayelekile pass ukuhlolwa, ikakhulukazi uma basengozini.
- Prevention syndrome hepatolienal ngokuyinhloko kuhlanganisa ekulweni izimbangela libangele isifo sesibindi kanye ubende.
- Qiniseka ukugcina Ukudla elifanele okune lemali edingekayo amafutha, amaphrotheni kanye carbohydrate, yebo, amavithamini.
- Musa ukuphuza ngokweqile, ukubhema futhi ahole indlela yokuphila enempilo.
Akukho izifo ayinangozi, ikakhulukazi uma iphathelene ezinjalo zomzimba ezibalulekile njengoba sesibindi ubende. Ukuthola Isikhathi esijwayelekile zezinkinga, bese ukuphathwa ezifanele bayakwazi ukunikeza imiphumela ngempumelelo.
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