ImpiloIzifo nemibandela

Anaemia aplastic

anaemia Aplastic kuyinto eziyinkimbinkimbi isifo igazi. Lihlobene nokubhekana ubuso ukukhiqizwa esincishisiwe granulocytes, izinhlayiya zegazi kanye egazi abomvu umnkantsha. amagama Medical libhekisela kokugula bacindezeleke lokhu hematopoiesis isifo.

anaemia Aplastic libhekene ukwehla sokuphila abomvu egazi, ephelezelwa ukubhujiswa egazi abomvu kumaseli umnkantsha phakathi nawo wonke amabanga ukuthuthukiswa.

Lesi sifo kunomthelela omubi kakhulu nokusebenza kwezitho eziningi. Ngakho-ke, izinyathelo ngesikhathi esifanele zokuxilonga kanye nokwelashwa afanele isifo kwakuyoba ngcono kakhulu izinga lokuphila.

anaemia Aplastic ingaqala ngasiphi yobudala. Kodwa ngokuvamile, ngokusho izibalo, nivame lesi sifo yilabo abaneminyaka engama amahlanu.

Imbangela yale isifo ayikaziwa cishe u-80% amacala.

Kungenjalo, ngokocwaningo ochwepheshe, mhlawumbe, isifo esibangelwa yizici zangaphandle, ezifana nokusetshenziswa nokunwetshiwe izidakamizwa (antibiotic, antituberculosis izidakamizwa, sulfonamides, neminye imithi antiinflammatory).

anaemia Aplastic iqhubeka ne ephefumula isikhathi eside mercury evala, amafutha, benzene compounds, kanye ngenxa yokuchayeka emisebeni.

Ezinye amacala isimo elihlobene ne ukuthuthukiswa izinqubo ezithathelwanayo emzimbeni, izinkinga ezahlukene ukusebenza omzimba futhi endocrine.

Izizathu ngenhla ochwepheshe bathi ifomu atholwe lesi sifo.

Imvelo lezinceku isifo livezwa kwezinhlobo eziningana.

Lesi sifo kungahluka ukuba khona noma ukungabi khona kahle kwezinso azalwa naso ekuthuthukiseni nge ukunqotshwa ingqikithi ukwakheka kwamangqamuzana egazi abomvu. Futhi, kukhona i-anemiya nge zokugula zikhethe.

Izimpawu zincike uhlobo isimo.

Izimpawu Fanconi anaemia kuyagcinwa ekuqaleni kuka ebuntwaneni. anomalies azalwa naso kuvetwa ukuthi wayenezinkinga ezinkulu nasezithweni ukuthuthukiswa ithambo izicubu (clubhand, inombolo ongaphelele iminwe isandla, njll). Ngesikhathi esifanayo kukhona jikelele ubuthakathaka, ubuhlungu bekhanda, ezifweni ukuba imikhuhlane. Ukuhlolwa kwegazi kwembula ESR okusezingeni eliphezulu. Njengomthetho, lokhu isimo uyaqhubeka kuze engu-nesishiyagalombili ebulalayo ngenxa ukutheleleka ngephutha noma ukopha.

Lapho anaemia Oestrich-Dameshek kwezinso kungekho azalwa nako. Lolu hlobo isifo kuyaqabukela uyalandelwa.

Ngo kwegazi, Diamond Black fan ezimweni ezingajwayelekile, kukhona ukulimala kwamehlo kanye skeleton. izimpawu ezivamile kulesi simo kukhona esikhumbeni luhlaza lemicu empunga elinamathela othini bese ubende lakhulisiwe. Ukuhlolwa kwegazi wembula -hemoglobin encishisiwe kanye ukwanda okukhulu kwezincwadi isilinganiso erythrocyte futhi leukocyte. Njengoba umkhuba ubonisa, iningi leziguli musa ukuphila ngokuvumelana engamashumi amabili.

Ngazuza acute isifo Yiqiniso kuyahluka emathunjini obuningi, izinso, acinene futhi isikhumba ukopha. Ngesikhathi esifanayo ukuthuthukisa imfiva.

Kwaphela izinsuku eziningana, iziguli babone ukwehla okukhulu ngo count platelet, kwamangqamuzana amhlophe egazi ne amangqamuzana abomvu egazi. Lokhu kuhlola kwembula okusithiyayo weseli nokuvuthwa nokwehliswa egazini. Ukufa kwenzeka cishe ngo ezine kuya kweziyisishiyagalombili amasonto.

ifomu Subacute libhekene ukopha ngaphansi ezinzima. Life kusukela ekuqaleni isifo ziyahlukahluka kusuka ezintathu kuya nantathu izinyanga.

Ifomu njalo lesi sifo ukugeleza kancane. It libhekene remissions eside.

In iziguli obusebenzayo esingamahlalakhona adrenal kwenzeka normocytic anaemia normochromic ngendlela emnene. Lesi simo kuyinto ezimweni eziningi ukuwazi eyanele, ngenxa ukwehla kanyekanye e zomthamo.

Ngenxa yalokho ukwephula yomsebenzi haematopoietic hepatic eba anaemia macrocytic.

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