Isifo Caroli sika: Izimpawu kanye Ukwelashwa

isifo Caroli sika ukuphazamiseka eziyinkimbinkimbi kakhulu sokusebenza kwesibindi, ukuxilongwa kanye nokwelashwa elibangela nobunzima obukhulu odokotela.

Siyini isifo

Caroli Izifo - ezingavamile isifo sesibindi azalwa naso okubangelwa ukunwetshwa Amapayipi Bile, etholakala ngaphakathi emzimbeni. Lubonakala ngalolo traffic evamile iphazamisekile Bile yokujama tsi kwenzeka futhi ukubusa yayo ukutheleleka. Ngokuvamile lesi sifo kuvamile amadoda, futhi iqala ebuntwaneni noma usakhula. Inqubekela phambili inqubo sokugembula incike lemali kanye degree of umonakalo Amapayipi ngaphakathi isibindi.

izinhlobo isifo

Kuze kube manje, i-ngezigaba esizimele isifo Caroli sika kwezokwelapha sishoda. Nokho, naphezu kwalokhu, kukhona izinhlobo ezimbili ezahlukene zesifo. Ifomu yokuqala ungachazwa ukuthi eziphukile patency biliary, lapho kumiswa okwalandela zamatshe.

Ifomu yesibili elihlobene ne azalwa naso cystic hepatic. Kulokhu, kukhona ukunwetshwa kancane Amapayipi kanye kumiswa amatshe kungenzeka, nakuba kungase ngezinye izikhathi zenzeka ezigabeni kamuva lesi sifo.

Advanced Bile Amapayipi kungase uxhumeke izindawo isibindi fibrosis futhi ngaleyo ndlela ibukeke oluncane ukuqina e simila inesikhala.

izimbangela

Caroli isifo kubhekisela esenzakalweni esiyisimangaliso izifo azalwa naso ezivukayo ngenxa autosomal imodi esikhubazayo yefa. Uma une eziseduze ne zokugula efanayo, ngemva kokuzalwa kwengane ngokushesha kudingeke aqhube luhlolo olunzulu, njengoba kukhona usethubeni kokudlulisela izifo sitholwa njengefa.

Kwezinye izimo, lesi sifo futhi belekelelwa iziyaluyalu sokugembula kwesibindi, okuyinto nzima kakhulu ekwelapheni.

Izimpawu main

izimpawu isifo Caroli angakwazi azibonakalisa ngokuphelele ibuphi ubudala e izingane kanye nabantu abasha. Kungenzeka ukuba sithwale izici eziyinhloko isifo ezifana:

• Ubuhlungu obukhulu besisu,
• umkhuhlane;
• yellowness okuncane kwesikhumba;
• isibindi ukwandisa ku palpation.

Make ukubonakaliswa emitholampilo ye isifo zivame ezihlobene okuvela ukuvuvukala. Ngokuyinhloko Caroli sifo sitholakale umuntu abantwana besilisa. Emhlanganweni exacerbation kuye kwabangela ukwanda okukhulu kwezincwadi ezingeni bilirubin nomhlophe cell segazi.

isevisi kuyinto

Naphezu kweqiniso lokuthi izimpawu zesifo ngokwanele esivezwayo, kodwa kubuye kube isici nezinye izifo isibindi. ukusazi ngokunembile isifo esikuphethe futhi ukunquma isifo kungenzeka Caroli e-United States futhi ngesikhathi CT. computed tomography kubhekwa eyodwa yezindlela kakhulu ulwazi of luhlolo, ngoba ungabona kahle ngokwanele zonke ukwephula imithetho. Ngaphezu kwalokho, cholangiography endoscopic Kungase kudingeke izinhlelo zokuphepha uphethwe.

Isibindi umsebenzi ukuhlolwa isikhathi eside akusho Nokho, ukushintsha ne ukuqhubeka kwesifo kanye isikhathi eside ukuvuvukala kule ukuhlaziywa kwamakhemikhali kwegazi kungathola zonke izibonakaliso cholestasis.

Ngenxa iziguli basengozini cholangiocarcinoma, ukwengeza kumele kwenziwe futhi Ukuhlolwa serological ngokuba khona isimila iziphambano.

Izici yokwelashwa

Ephambi kwezinduna Caroli isifo eziqondisweni zokwelapha kufanele kuqashelwe nakanjani, ngoba lokhu zokugula kuchubekele embili ngokwemvelo. Ukwelashwa kusho isicelo of imithi ebulala izinhlobonhlobo zamagciwane, futhi ursodeoxycholic isimo acid ekuphathweni ukuvimbela calculus kumiswa.

Ngaphezu kwalokho, ukuphathwa yakhiwa:

• analgesics;
• amatshe litholysis;
• amanzi biliary.

Lapho ukubusa, cholangitis, noma nezinye izinkinga yokwelapha ubovu akuhlukile ekwelapheni cholangitis virus. Kubalulekile ukususa ubomvu bese uhlanzekile Kwenziwa we imbobo Bile, futhi kusetshenziswe imithi elwa namagciwane ukusiza ukususa ukutheleleka.

Ukusebenza wenziwa kuphela endabeni exacerbations njalo noma ukusetshenziswa ayizwakali izindlela zokuthwebula izithombe zokwelapha olandelanayo. Umthamo kokungenela kuhlinzwa ingahluka kakhulu. amatshe kuphela noma amavesi biliary kungaba zisuswe.

Endabeni enamandla kakhulu amavesi ukuwathuthukisa biliary Bile yokujama tsi, udokotela ohlinzayo ukuraga ukususwa eyodwa Lobe kwesibindi. Ezimweni ezimbi kakhulu, esingamahlalakhona hepatic e khona noma izimpawu ukonakala ku isimila esibulalayo, ukufakelwa isibindi kungenzeka Kunconywa kusuka esiseduze.

Ukuze uthole imiphumela emihle, odokotela abaningi batusa ukuchitha ezinye kwezitho isibindi ngisho nalapho engekho izimpawu ezinamandla emabangeni kokuqala kwalesi sifo. Nokho, ngokuvamile, khona ukutheleleka kuyinto contraindication ukuze ukufakelwa. iziguli isilinganiso lokusinda emva ukufakelwa cystic azalwa naso eziye ngaphezu kwalokho kwatholakala ukuthi nginesifo cholangitis phakathi kwezitho, kunalokho ongaphakeme.

Izibikezelo yalesi sifo ngempela okungekuhle, kusukela umuntu angase ashelele phezu kweminyaka eminingana. Nokho, kakhulu kuyaqabukela kuphumela ukufa isiguli.

Caroli isifo

Caroli Izifo kaningi elihlobene ne azalwa naso cystic hepatic, kuphumele i isifo Caroli. Zombili lezi pathologies akhiwa kucishe ifomu biliary iziyaluyalu kwezicubu isibindi ezingeni yentuthuko sombungu. Lesi yisifo ngofuzo nesihlobo esiseduze kanye wabonakaliswa ubuhlungu besisu futhi opha varices ngomphimbo. Neonates kungaba inhlanganisela izimpawu eyinhloko azalwa naso cystic hepatic, Caroli isifo futhi polycystic nesifo sezinso.

Lesi sifo libhekisela azalwa naso Bile imbobo simila, Nokho, kunzima kakhulu ngendlela engavamile futhi kukhona ikakhulu abantu abaneminyaka engaphansi kwengu-30. Eminyakeni embalwa yokuqala zokugula kwenzeka cishe asymptomatic, inqobo nje ukunwetshwa Amapayipi Bile musa avuse yokujama tsi of Bile, okuzodala nemibandela kumiswa amatshe futhi ukubusa ukutheleleka. Uma isetshenziswa kanye nezinye izimpawu waphawula ka-jaundice, kubonisa khona cholangitis.

It kugujwa ukulimala kwesibindi ikakhulu kwesokunxele emaceleni, kodwa kungase futhi kube indlela ezimbili kwezinye izimo.

Kwezinye izimo, isibindi yakhe sinamandla kakhulu kangangokuba kungangena nezinye izitho. Ngakho omunye yezinkinga kubhekwe njengento okuvela ukwehluleka kwezinso.