Ikhaya NomkhayaSokukhulelwa

USIZO syndrome (HELLP-syndrome) - kwetintfo eziyingozi III senyanga yokukhulelwa: izimbangela, uphethwe, ukuphathwa

Emphilweni wonke umuntu nakanjani oza umzuzwana ukuthi amabutho ukuba baphendukele usizo ngaphandle. Ngokuvamile abasizi ezimweni zinjalo abezimo eziphuthumayo. Lokhu kwenzeka uma umzimba womuntu yahlasela isifo kunganakekile, futhi ubhekane nazo akunakwenzeka. Wonke umuntu uyazi ukuthi isimo esijabulisayo sokukhulelwa - akusona isifo, kodwa ukuthi omama esizayo isidingo oluthile usizo lwezokwelapha nezingokwengqondo.

"Siza!", Noma lapho igama isifo

Call usizo ngezilimi ezahlukene umsindo ezahlukene. Ngokwesibonelo, ngesiNgisi a yenza ngokuphelelwa yithemba isiRashiya, "Usizo" Ingabe liphinyiselwe efana "USIZO". USIZO syndrome (HELLP) cishe ngengozi uvumelane ngalesi sicelo manje ngamazwe usizo.

Izimpawu kanye nemiphumela yalesi inkinga ngesikhathi sokukhulelwa yokuthi ukunakekela kokulashwa okusheshayo kubalulekile. HELLP segama lahlukene izinkinga zezempilo: esibindini, ngegazi ekunqandeni futhi babe sengozini enkulu yokufa ukopha. Ngaphandle kwezinto ezibalwe ngenhla, HELLP-syndrome kubangela ukungasebenzi nezinso blood pressure iziyaluyalu, kanjalo ibe yimbi kakhulu inkambo sokukhulelwa.

Isithombe lesi sifo sinzima kangaka ukuthi kukhona lelicala Iqiniso ukuzala umzimba, ukwehluleka sokuhlasela kwamasosha omzimba kwenzeka. Lokhu kwenzeka lapho sindisa ingqikithi umzimba female lapho izivikelo senqabe ukusebenza, Rolls ukucindezeleka olunzima, lantambama ngempilo izimpumelelo aqhubeke nomzabalazo. Igazi akusho ihlule, isilonda akamphulukisanga, ukopha akagcini nesibindi akakwazi ukwenza imisebenzi yaso. Kodwa kungcono isimo esibucayi amenable ukusolwa wezokwelapha.

nemlandvo wetekwelashwa

USIZO syndrome achazwa ngasekupheleni kwekhulu le-19. Kodwa kuphela ngo-1978 Gudlin ngabophela zokugula sokuhlasela kwamasosha omzimba pre-eclampsia ngesikhathi sokukhulelwa. Futhi ngo-1985, sibonga Weinstein, izimpawu disparate aye ahlanganiswa namanye ngaphansi igama elilodwa: HELLP-syndrome. Kuyaphawuleka ukuthi imithombo yezokwelapha yasekhaya, lokhu kuyinkinga enkulu cishe hhayi kuchazwe. ezimbalwa kuphela anesthetists Russian nokunakekela Ochwepheshe olunzulu ahlinzeke ngemininingwane eminingi ngokusondelene adiliza le isimo esibucayi of preeclampsia.

Phakathi naleso sikhathi, u-SIZO syndrome ngesikhathi sokukhulelwa ngokushesha ikhula ngesivinini, alisuse eziningi izimpilo.

Sichaza inkinga ngayinye ngokwehlukana.

hemolysis

USIZO syndrome ngokuyinhloko kuhlanganisa intravascular hemolysis. Lokhu nobulwelwe libhekene ekubhujisweni ngokuphelele esitokisini. Ukubhujiswa nokushwabana kwamangqamuzana egazi abomvu kubangela imfiva, jaundice kwesikhumba, ukubukeka igazi izifundo umchamo. Imiphumela ezisongela ukuphila kakhulu - ingozi ukopha esindayo.

Ubungozi thrombocytopenia

Uphiko esilandelayo nezifinyezo syndrome - thrombocytopenia. Lesi simo libhekene ukwehla platelet count ifomula wegazi, ekugcineni kubangela ukopha nokuguqulwa. Misa le nqubo kungaba esibhedlela, futhi ngesikhathi sokukhulelwa, kulesi simo kuyingozi ikakhulukazi. Isizathu kungaba iziyaluyalu ezinzima mzimba, okwaholela anomaly lapho umzimba elwisana ne ngokwayo, abhubhise amaseli enempilo legazi elibomvu. Limelela usongo ekuphileni wasuka ku isizinda izinguquko inani zegazi ekunqandeni iziyaluyalu.

kuzalwa Kubi: ukwanda enzyme isibindi

I pathologies eziyinkimbinkimbi kufakwe USIZO syndrome, ebekiwe umqhele ezifana uphawu ezingemnandi njengoba enzyme isibindi anda. Ukuze omama abakhulelwe okusho ukuthi kwelinye izitho ezibaluleke kakhulu zomzimba womuntu kukhona amaphutha abo angathi sina. Phela, isibindi ehlanza hhayi kuphela umzimba ubuthi futhi usiza ukuqaliswa umsebenzi wokugaya ukudla, kodwa sithinta sphere psycho-ngokomzwelo. Ngokuvamile ezifana ushintsho engathandeki itholwa phakathi kwegazi isimiso, elawulwa ukuze owesifazane okhulelwe. Lapho preeclampsia nzima syndrome USIZO izibalo kuhluke kakhulu kusuka kuyinsakavukela, kuveze isithombe onaso. Ngakho-ke, lodokotela - inqubo yokuqala, okuyinto esiyisibopho ukuba abantu babulawelwe kuzo.

Ikakhulukazi yokuthathu yesithathu

3 senyanga yokukhulelwa kubaluleke kakhulu ngoba ikusasa lalowo sokukhulelwa kanye kwezidingo. yezinkinga njalo kukhona edema, isilungulela ukungasebenzi wokugaya ukudla.

Lokhu kwenzeka ngenxa ukushayisana nezinso isibindi. kwesibeletho lakhulisiwe ayinakho ingcindezi elihlekayo ku ngokweqile, izitho zokugaya, okuyinto kungani Sebeyeza sicacise. Kodwa ngo gestosis ezingase ziphakame isimo ngokuthi zangaphambi eclampsia futhi eclampsia, okuyinto babhebhethekise ubuhlungu epigastrium, avuse ukubukeka isicanucanu, ukuhlanza, edema, umfutho wegazi ophakeme. Against ngemuva yezinkinga zezinzwa singenzeka nokuquleka. izimpawu eziyingozi ukwandisa, ngezinye izikhathi cishe njengombani uvela, enza umonakalo omkhulu emzimbeni, kusongela impilo umama okhulelwe futhi ingane. Ngenxa preeclampsia ezinzima, okuvame ihambisana 3 senyanga yokukhulelwa, kuvame kuba syndrome nesikhulumi ngokuthi USIZO.

izimpawu elikhanyayo

HELLP-syndrome: isithombe yomtholampilo, ukuxilongwa, amacebo azoya - isihloko ingxoxo kwanamuhla. Okokuqala, udinga ukukhomba eziningi izimpawu eziyinhloko ezihambisana lokhu inkinga esabekayo.

  1. On the ingxenye isimiso sezinzwa esiyinhloko. Isimiso sezinzwa aphendvule lezi nokuquleka iziyaluyalu, ikhanda okukhulu, ongaboni.
  2. Jobe esimiso senhliziyo nemithambo yegazi kuyaphazamiseka ngenxa edema kwezicubu futhi kwehle kwegazi.
  3. izinqubo zokuphefumula ngokuvamile umthetho, kodwa edema yamaphaphu, zingaba khona ngemva kokubeletha.
  4. On the ingxenye hemostasis futhi thrombocytopenia waphawula ukwephulwa of platelet ingxenye ukusebenza umsebenzi.
  5. Encishisiwe kokusebenza kwesibindi, ngezinye izikhathi ukufa amaseli ayo. Akuvamile waphawula nokuguqulwa ukudabuka hepatic, okuholela ekufeni.
  6. Ukwephula uhlelo genito-urinary: oliguria, ukungasebenzi kwezinso.

USIZO syndrome elinesimo izimpawu ezinhlobonhlobo:

  • ukungakhululeki esibindini;
  • ukuhlanza;
  • bekhanda acute;
  • ukuquleka;
  • isimo okunomkhuhlane;
  • ukuphazamiseka ukwazi;
  • esingamahlalakhona urinary;
  • izicubu edematous;
  • ingcindezi okungajwayelekile;
  • nokopha amaningi ezindaweni zokukhwabanisa;
  • yellowness.

isifo Laboratory livezwa thrombocytopenia, hematuria, lo ukuthola of amaprotheni ku umchamo futhi igazi, i-hemoglobin ongaphakeme, ukwanda kokungabi bilirubin ekuhlolweni igazi. Ngakho-ke, ukucacisa kuyodingeka uphethwe eqondile yonke ukuhlolwa laboratory eziyinkimbinkimbi.

Indlela ukuqaphela lezo zinkinga?

Ukuze ngesikhathi esifanele ukuthola ukuvimbela yezinkinga ezinzima, futhi kwenziwe lodokotela lapho mums esizayo belulekwa ukuba sifike njalo. Uchwepheshe abakhulelwe esegqoka irekhodi, bese eduze nokuqapha izinguquko emzimbeni womuntu wesifazane phakathi nayo yonke inkathi. Ngakho, udokotela wezifo zabesifazane ngesikhathi esifanele silungise ngeziphambeko engadingeki futhi uthathe isinyathelo esifanele.

Kuze phendla izinguquko sokugembula ngokusebenzisa ukuhlolwa laboratory. Ngokwesibonelo, amaprotheni umchamo kuzosiza ukuthola uma ikhona. Ukwanda amaprotheni izinkomba kanye nenani leukocyte kusikisela semfene evelele emsebenzini nezinso. Phakathi kwezinye izinto, bangase inciphe elibukhali inani umchamo, kanye nokwanda okuphawulekayo edema.

Izinkinga esibindini ziyabonakala hhayi kuphela ngaphezulu ngakwesokudla quadrant ubuhlungu, ukuhlanza, kodwa futhi ushintsho egazini (kwenyuke amanani enzyme kwesibindi), futhi isibindi ukwandisa ku palpation esiyitholayo ngokucacile.

Thrombocytopenia nayo ukutholwa laboratory ivivinya igazi nokuthumba owesifazane owayezithwele, okuyiwona buyingozi USIZO syndrome.

Uma usola ukulawula eclampsia kanye USIZO syndrome saziso wegazi ngenxa spasm yegazi kanye amahlule ukusebenza kwakhe kungandisa sina.

ukuxilongwa umehluko

Imfashini kulezizinsuku HELP syndrome uphethwe ngo zokubelethisa uye kwakuqala ukwanda, ngakho ngokuvamile wakubeka ngephutha. Ngokuvamile ukufihla ngemuva ke kukhona izifo ezahlukene ngokuphelele, hhayi kancane esiyingozi, kodwa ezivamile kakhulu futhi evamile:

  • kolwelwesi;
  • ukusha kwesibindi kohlobo viral;
  • omzimba izicubu erythematosus;
  • urolithiasis;
  • sepsis azoya;
  • izifo kwesibindi (okunamafutha, isifo sokusha);
  • purpura thrombocytopenic of omsakazo engaziwa;
  • nokwehluleka ukusebenza kwezinso.

Ngakho-ke umehluko. Sifo kufanele inake ezihlukahlukene ongakhetha. Ngenxa yalokho, kukhonjisiwe ngenhla triad - hyperenzymemia isibindi, hemolysis futhi thrombocytopenia - ngaso sonke isikhathi kubonise khona kwale inkinga.

Izimbangela USIZO-syndrome

Ngeshwa, engcupheni bengayiqondi kahle, kodwa kukhona iziphakamiso ukuthi kumkhathaze USIZO syndrome zingase kube ngenxa yezizathu ezilandelayo:

  • izifo zengqondo;
  • izidakamizwa olubangelwa ukusha kwesibindi kohlobo;
  • izinguquko zofuzo enzymatic esibindini;
  • prolificacy.

Ngokuvamile syndrome yingozi kwenzeka uma ukunaka enganele preeclampsia nzima Yiqiniso - eclampsia. Kubalulekile ukwazi ukuthi lesi sifo liziphatha ezingalindelekile kakhulu: it is asathuthuka ngejubane lombane, ithathe iphele kwayona.

izinyathelo zokwelapha

Lapho lonke uvivinyo eyenziwa kanye umehluko. Imiphumela yaloku kuhlola okungenhla, ungenza eziphethweni eziqinisekile. Lapho ufaka uphethwe "USIZO syndrome" impatho okuhloswe ngaso eliletha ukuthula isimo owesifazane okhulelweyo umntwana ongakazalwa, kanye ukulethwa ngokushesha izimele kwethemu. imisebenzi yezokwelapha abazenzi ngosizo i Udokotela Wabesifazane, iqembu yokusiza umuntu ukuba aphefumule, lo obulala izinzwa. Uma kudingekile, xhuma nezinye Ochwepheshe: kudokotela oyisazi sezinzwa ngezindleko noma ophthalmologist. Ngokuyinhloko iqedwe lezo zitho zomzimba eziningi, futhi enikeziwe izinyathelo zokuvimbela ukuze ligweme izinkinga ezingase zivele kungenzeka.

Phakathi ezivamile nzima inkambo kokungenela yezokwelapha, bungabonakala:

  • lamabutho esinomhlapho;
  • ukopha;
  • ubuchopho edema;
  • edema yamaphaphu;
  • ukwehluleka oyingozi kwezinso;
  • izinguquko isibindi ebulalayo futhi igebe;
  • ukopha okungenakudanjiswa.

Lapho okuyikona futhi ifike ngesikhathi esinikeziwe usizo lochwepheshe ukuze amathuba abagulela ukufa ivame ukuba ubuncane.

isu azoya

Amaqhinga wayekwenza zokubelethisa maqondana amafomu okunzima preeclampsia, kulapho eziyinkimbinkimbi syndrome USIZO, licacile: ukusetshenziswa Ukubeletha. Lapho abavuthiwe kwesibeletho ngomumo sokubelethisa zemvelo, usebenzisa prostaglandins noyisibopho epidural.

Ezimweni ezimbi kakhulu, Ukubeletha isetshenziswa izinzwa kuphela endotracheal.

Life emva kokubeletha

Ochwepheshe kuqashelwe ukuthi isifo kwenzeka ngesikhathi senyanga yesithathu hhayi kuphela, kodwa futhi ikwazi ukuthuthuka ezinsukwini ezimbili emva ukususa umthwalo.

Ngakho-ke, HELP syndrome emva kokuzalwa - lo mkhuba kungenzeka ngempela ukuthi ukhuluma esivuna ukuqapha eduze kukanina ingane esikhathini kwangemva kokubeletha. Ikakhulukazi kumayelana besifazane kakhulu ogeleza preeclampsia ngesikhathi sokukhulelwa.

Ubani obangela futhi yini okufanele uyenze?

USIZO syndrome - kuphazamisa cishe zonke izinhlaka futhi izinhlelo zomzimba zesifazane. Phakathi isifo kukhona outflow kakhulu nobungqabavu kanye awokuthi ukufa, futhi intrauterine kwezinso fetus. Ngakho-ke, kusukela 20 ngesonto th of umama okhulelwe kubalulekile ukuqhuba self-ukuqapha idayari, okuyinto ukuletha zonke izinguquko ezenzeka emzimbeni. Ngokukhethekile kufanele kukhokhelwe la maphuzu alandelayo:

  • wegazi: ke kuzuba phezulu izikhathi ezingaphezu kwezintathu kufanele wazise;
  • isisindo yokuguqukela kwesinye isimo: uma engayifezi kahle avuke ngokucijile, mhlawumbe, isizathu ukuthi kwaba ukuvuvukala;
  • ukunyakaza kwengane okukhulu kakhulu, noma, Ngakolunye uhlangothi, ukunyakaza nzonzobala - ngokucacile isizathu ukwelashwa udokotela;
  • khona edema: bese kuba khona ukuvuvukala esikhulu kwezicubu kusikisela ukungasebenzi kwezinso;
  • engavamile ubuhlungu esiswini: abalulekile ikakhulukazi endaweni kwesibindi;
  • ukuhlaziywa njalo konke qobo oqokiwe, kufanele wenziwe ngokwethembeka okuhle futhi ngesikhathi, njengoba kufanele kube ukuze kuzuze wona kanye kukamama nengane engakazalwa.

Zonke izimpawu eziyisixwayiso kufanele ngokushesha kubikwe kudokotela wakho, udokotela wezifo zabesifazane njengoba bakwazi kuphela ngokwanele ukuhlola isimo futhi ukuthatha isinqumo esifanele.

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