Impilo, Izifo nemibandela
Madelung syndrome: izimbangela, izindlela ukwelashwa kanye nokuvimbela
kwesilevu Double - isici ukuthi kungenzeka ukuthi umataniswe nge umzimba thuthuva noma ikhuluphele ngokweqile. Ngezinye izikhathi kungcono nje isici umzimba. Kodwa kwezinye izimo, ukwanda okusheshayo e nenani fat umzimba - ubufakazi isifo esiyingozi Madelung. Lesi sifo kungaba kuphila kwetfu engotini, kodwa iholela ukuthuthukiswa izakhiwo ngokwengqondo.
Izici lesi sifo
Lipomatosis uhlobo isifo Madelung sika. Syndrome kungenxa ukuhlukumeza izinqubo umzimba emzimbeni, kangangokuba amanoni isakazwa kahle, kukhona ezifakwa elikhulu endaweni entanyeni.
Ngokokuqala ngqá sifo achazwa 1888 by Madelung udokotela - kungakho igama layo liyi ezifanele.
Ngokwezinga elikhulu obala isifo abantu abadala besilisa nabesifazane. zokugula Pediatric cishe hhayi sitholakale.
izizathu
Kungani ukuthuthukisa Madelung (syndrome)? Impendulo ngqo kulo mbuzo namuhla, akekho ikani. Nokho unikeze inombolo yezinto ezingaba nomthelela zokugula:
- Lena ufuzo kuyiqiniso ngokukhethekile. Uma zokugula ebonwe uyise noma unina, kukhona amathuba afanayo fat umzimba ngesikhathi ube neminyaka ethile ubudala futhi ingane.
- Ngaphezu kwalokho, isibangeli sokuthuthukiswa sifo kungaba iziyaluyalu hormone emzimbeni.
- Iqembu ingozi kuhlanganisa nabantu izidakamizwa notshwala umlutha.
- Ukwephula izinqubo umzimba emzimbeni kungabangela ukunqwabelana sindisa kwemizwa nokucindezeleka. Ngokuvamile lipomatosis, kuhlanganise Madelung syndrome, ukwelapha esidinga indlela ekhethekile, sitholakale abesifazane ababeka njalo ahlale phezu ukudla. Ngenxa okungafanele Ukudla amafutha iqala lihlehle, hhayi lapho kudingeka.
symptomatology
Ekuqaleni, isiguli ngigcine lwezimpawu eziningi fat entanyeni zamanzi. Ngeshwa, ngalesi sigaba, bambalwa kakhulu abantu inamathela ukubaluleka izimpawu ezingemnandi ngaphandle befuna usizo lodokotela. Kwaphela izinyanga eziningana entanyeni kungase kwandise kakhulu ngobukhulu. Umphumela iphika ubuhlungu.
Uma kukhona isici ngofuzo, kubalulekile ukufunda imininingwane mayelana Madelung syndrome. Ukwelashwa futhi izimpawu, zokuvimbela izindlela - konke lokhu kwaziswa kubaluleke.
ekwelapheni lesi sifo
Lokubaluleke kakhulu yikona esifike ngesikhathi evumela ukunquma isizathu esenza ekuqaleni ngokushesha sikhule izicubu fat. Ngokolwazi etholwe, uchwepheshe esabela yokwelapha ehlanganisa ama-hormone disintoxication nezidakamizwa eqeda ukuvuvukala. Kodwa kusukela ezinkulu wen ngeke ukwazi ukuqeda ngaphandle kokuhlinzwa, ngakho isiguli ilungele ukuhlinzwa.
kubhekwa endoscopic ukususwa lipomas Ngaphansi kuhlasimulise entanyeni. Nokho, le ndlela kufanelekile kuphela uma une ezifakwa elincane amafutha. Ngasese umkhuba imitholampilo kanye nezinqubo kuhlinzwa usebenzisa laser.
Ngeshwa, ukukhishwa izimila benign asiqinisekisi ukuthi kungayi lubuyayo Madelung Syndrome esikhathini esizayo. Ukuvimbela yokuphindela efanayo ukugwema ngokweqile ukudla okunamafutha kanye notshwala, kanye ngokuziphatha ngendlela enempilo bebonke. Ngokushesha ukwelapha lesi sifo sizokwazi uma ukufuna usizo ngendlela efanele usaqala.
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