ImpiloIzifo nemibandela

Isifo Berger sika (Iga-nephropathy): izimbangela, ukwelashwa

isifo so-renal zenzeka kaningi. Lezi zihlanganisa izifo ezifana pielo- futhi glomerulonephritis. Ngaphandle kwalezi, kukhona nezinye izifo kohlelo urinary. Omunye wabo isifo Berger sika. Lokhu zokugula, futhi, libhekisela anomalies njalo. It sitholakale cishe u-20% amacala of isifo sezinso ezingabantu. Lokhu ukuhlukumeza awasebenzi kuphela izinkinga Nephrology, njengoba kuyinto ukuthuthukiswa mshini mzimba. Usola lokhu zokugula singaba uphawu main - hematuria okwedlulele.

isifo Berger sika - kuyini?

Lesi sifo kuwuhlobo glomerulonephritis ezingamahlalakhona. Kuqhathaniswa unesifo sikashukela nephrotic samuntu zamanje, isifo Berger sika has a Izibikezelo ezinhle. Naphezu kweqiniso lokuthi ke sitholakale esemncane (iminyaka 15-30), ayivamile kube kubi nakakhulu esingamahlalakhona kwezinso. I ukubonakaliswa oyinhloko sifo - lena hematuria okwedlulele kanye nokuhlukumezeka esifundeni lumbar. Lokhu zokugula ungakwazi futhi zenzeka izingane. Ngo kwabesilisa livela izikhathi 4 kakhulu ukudlula abantu besifazane. Njengoba nazo zonke pathologies, uphethwe i-International Ukwahlukanisa Diseases (ICD). Nephropathy Berger N02 inekhodi, okusho "i-hematuria ozinzile futhi yansukuzonke."

Izimbangela zesifo

Imbangela eyinhloko isifo kuyinto inqubo ezithathelwanayo. Ezimweni eziningi zokugula kwezinso eba ngemva izifo ezibangelwa amagciwane kanye ezibangelwa amagciwane. Futhi, Imbangela kungase kube isifo fungal. Izimpawu ezivame ukubonakala ngemva kwezinsuku ezimbalwa ukutheleleka kwadamba phezulu ipheshana zokuphefumula (sibi zokuphefumula igciwane lohlobo, umphimbo obuhlungu, pharyngitis). Imbangela ngokushesha lesi sifo ukunqwabelana izakhiwo mzimba ezindongeni kwezinso semithambo. Kwezinye izimo, ukuxhumana zokugula abadliwa umlando lezinceku (ngofuzo Iga-nephropathy). Ngaphezu kwalokho, lesi sifo lihlotshaniswa yofuzo. Ukwabela izimbangeli ezilandelayo:

  1. Ukungenwa amakhaza.
  2. Kwehliswe amasosha omzimba.
  3. izinqubo Okungalapheki ezibangelwa amagciwane kanye ezibangelwa amagciwane e yomoya engenhla.

Mshini yesifo Berger sika

I pathogenesis lesi sifo elihlobene ne sebethule izakhiwo mzimba ezindongeni umkhumbi. Ngo evamile izinso glomerular apharathasi unesibopho okufika igazi. Siqukethe sebuningini izitsha nephrotic. Ngemva ukutheleleka izakhi odlule ukuvuvukala - izakhiwo mzimba - emzimbeni futhi zibekwe apharathasi glomerular. Ngenxa yalokho, ukuthuthukisa glomerulonephritis. izitsha kwezinso ayikwazi ukusebenza ngokujwayelekile ngenxa izakhiwo umzimba ezifweni, nemithi igazi filtration siyabhubha. Ngaphezu kwalokho, ukuvuvukala kubangela ukunqwabelana uketshezi (edema parenchyma) futhi kunciphisa permeability we ulwelwesi engaphansi. Ngenxa yalokho, ukuthuthukisa hematuria macro- futhi ezincane. Izizathu lezi zinqubo kangakanani umonakalo glomerular futhi Ukungena ketshezi (igazi) ngokusebenzisa ulwelwesi engaphansi.

Ayini ngezimpawu zesifo kuyagcinwa e Berge?

Isithombe basemtholampilo isifo Berger sika sifana glomerulonephritis oyingozi. Noma kunjalo, kubalulekile ukuba bahlukanise phakathi lezi zifo ndawonye. Imbangela glomerulonephritis ngokuvamile igciwane staph. Nezindlela ezahlukene yokwelapha lezi zifo. Izimpawu eyinhloko Ig A-nephropathy yilezi:

  1. Hematuria. Ngokuvamile, lokhu kuyisibonakaliso sokuphoqa iziguli usizo. hematuria Gross kusho ukubukeka igazi e umchamo. Lokhu ngokuvamile ehambisana nobutha emizweni ezingezinhle.
  2. Microhematuria - ke kuwuphawu okungukuthi imperceptible kumuntu futhi wembula kuphela amasampula ekhethekile.
  3. Ubuhlungu esifundeni lumbar. Ngokuvamile, zingabantu ngiyaqaqanjelwa buthuntu nemvelo. Ngokungafani nezinye izinqubo ukuvuvukala kule izinso (pyelonephritis), ukungakhululeki waphawula nhlangothi zombili.
  4. Ukuba khona engenhla zokuphefumula ipheshana ukutheleleka ngaphambi.
  5. Ukwandiswa nezinga lokushisa komzimba.
  6. ubuthakathaka Jikelele.
  7. Proteinuria - ukubukeka amaprotheni ku umchamo. Kuyaqapheleka ku Ezimweni ezingavamile lapho inkambo atypical lesi sifo.

Sifo Ig A-nephropathy

The main umbandela zokuxilonga isifo Berger sika luyisifundo ezingamahlalakhona. izimpawu isiguli kuvame bakhathazekile izikhathi 2-3 ngonyaka emva kokutheleleka. Kubalulekile futhi ukwazi ukuthi lesi sifo kungavamile ukuba ingozi. Naphezu hematuria ngezikhathi ubonakalisiwe, kwezinso uhlala evamile. Ngokungafani nezinye izinqubo ukuvuvukala (pielo-, glomerulonephritis), isifo CRF Berger sika ezingavamile.

Laboratory uphethwe kuhlanganisa Kla OAM akhethekile amasampula umchamo (nechyporenko, Zimnitsky). Badinga ukuhlonza abomvu egazi kanye amangqamuzana amhlophe egazi. Kuye lokhu micro ukukhululwa kanye hematuria okwedlulele. Ngokuvamile, ukuhlaziya amaprotheni umchamo kungaba samanje. Ukuze uhlole ukuthi kukhona kungukuphula umsebenzi kwezinso, isiguli kufanele banikele ngegazi kusukela umthambo oyisazi samakhemikhali ezinto eziphilayo. Kulesi ukuhlaziywa, kubalulekile ukwazi ezingeni creatinine, futhi lokho kuyinto ejwayelekile lapho Berger isifo. Ukuze wafaka le uphethwe wokugcina, ucwaningo olwenziwe ngoba khona Ig A egazini. Ezimweni ezingavamile a biopsy izinso, lapho izakhiwo mzimba atholakala kudivayisi semithambo. Ultrasound nakho kuyenziwa ukuze kuhlonzwe umehluko.

Immunological ukuvuvukala kwezinso: ukwelashwa

Naphezu Yiqiniso ingozi lesi sifo ngesikhathi yokwelapha lokubuya kwesifo kuyadingeka. Kuyadingeka hhayi kuphela ukudambisa ngezimpawu zesifo, kodwa futhi sinombono ekuvimbeleni yezinkinga nasekusindiseni nokusebenza kwezinso. Ukwelashwa iqala nge yokulungiswa foci ukutheleleka. Ezimweni eziningi lokhu Nemithi Elwa Namagciwane (izidakamizwa "amoxicillin", "Cefazolin") kanye nama-ejenti elwa namagciwane (ukuthaka imithi "Viferon", "Genferon"). Ngaphezu kwalokho, ukwehlisa ukuvuvukala kule ama-NSAID izinso glomerular apharathasi ezidingekayo. izidakamizwa "Kanefron" zivame kakhulu ezisetshenziswa, "ibuprofen". Lapho isifo sezinso kukhona imithi ngempumelelo ukuthi zisekelwe amakhambi. Zimise zezinkambi akhethekile infusions (knotweed, birch efihlekile, bearberry).

Uma lesi sifo kunzima ukuyelapha, babe recurrences njalo noma izinkinga, bese ukuchitha yokwelapha i-hormone. Ngokuvamile linqume izidakamizwa "Prednisolone", namanxusa cytostatic. Kwezinye izimo, nokwelapha antiplatelet, indlela yokuthuthukisa ukugeleza kwegazi (izidakamizwa "Kurantil").

Ukuvimbela isifo Berger sika

Kufanele kukhunjulwe ukuthi isifo Berger sika siphathelene pathologies ezingamahlalakhona. Ngakho-ke, ukuze ugweme exacerbations, izinyathelo zokuvimbela kufanele sigcwaliswe. isikhathi Ezibalulekile sanitize lo foci ukutheleleka (namathansela, sinusitis), babe sesimeni hypothermia. Futhi, iziguli kufanele kube njalo herbal imithi izifundo, ukusekela amasosha omzimba.

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