Gunther isifo - kuyini?

Kukhona ososayensi zanamuhla sina akholelwa ukuthi zonke izindaba eyayisekhanda lami abe kwezesayensi. Babekwazi babe ngaphansi kwethonya leso sifo ezingavamile njengoba isifo Gunther noma "porphyria cutaneous." Lesi sifo olonakalisayo igazi, ukudala abahluphayo kabusha gem. Kukholakala ukuthi isifo Gunther kwakungu ezivamile emizaneni elincane eTransylvania. Kukhona-ke kuphakama kusukela nezokuxhumana ezihlobene eduze.

Ochwepheshe bathi uma hhayi lesi sifo, akasoze kukhona izindaba ezikhuthazayo nezinganekwane ka eyayisekhanda lami, Dracula kanye namanye amaqhawe nge fangs. Cishe zonke nesineke asymptomatic ngubani isiqalile kakhulu isifo Gunther sika - ejwayelekile vampire movie.

Thola imbangela yenkinga, futhi ukuchaza isifo ayengakwenza kuphela ekhulwini lama-20. Ngaphambi lokhu wathwalwa ubhekene nempi yangempela ne eyayisekhanda lami: kusukela 1520 kuya 1630 eFrance kuphela abhubhise abantu abangaphezu kuka-30 eziyinkulungwane, ababebhekwa njengezibonelo eyayisekhanda lami. I ujule ezweni kwavela ubuKristu, bayanda okwalapha ayephatha ngayo abantu abakwazi ukunqoba ngasekupheleni porphyria cutaneous.

Kusukela leli fomu ezingavamile isifo esidluliselwa ngofuzo ahlupheke umuntu oyedwa kuphela ngamunye izinkulungwane 200. Kulokhu, uma inkinga enjalo iyahlupheka omunye wabazali, ukuze kamuva sikhulume mayelana 25% ngokuqiniseka ukuthi isifo Günther sika-manifest kanye nengane.

Kukholakala ukuthi lesi sifo - umphumela ukulalana kwezihlobo. Medicine uchaza mayelana 80 amacala porphyria acute lapho kwakungenakwenzeka ukwelapha. isifo Gunther sika libhekene yokuthi umzimba akubi nemiphumela Izingxenye ezisemqoka igazi - abomvu egazi. Futhi lokhu kubonakala lapho kuntuleka yensimbi nomoya-mpilo egazini.

Ngo izicubu negazi kungukuphula sombala umzimba futhi ngenxa ukukhanya kwelanga kuqala iba yingxenye yomhlabathi-hemoglobin. Ngaphezu kwalokho, le nqubo kwenzeka umsipha nzima ukuthi kuholela curling yeminwe kwezinye izimo.

isifo Gunther sika libhekene yokuthi amagugu (non-amaprotheni ingxenye-hemoglobin) uguqulwe into enobuthi, okuyinto angase adle nezicubu ongama. Ngenxa yalokhu, isikhumba kuba nsundu ngombala, thins futhi amakhefu emva wenza elangeni. Ngenxa yalesi sizathu, ngokuhamba kwesikhathi isikhumba ezimboziwe ngokuphelele izilonda kanye nezibazi. Ngaphezu kwalokho, yisishiso kulimaze izindlebe nekhala, kanzima deforming kubo.

Ake ucabange ngendoda nge izinzwane curled nobuso embozwe izilonda ... scary Ngempela? Iziguli ezinjalo nje contraindicated kwelanga, ngoba lapho kubenza bahlupheke kakhulu. Isikhumba, etholakala emhlabeni izinsini izindebe some futhi yomile. Ngenxa yalokhu phansi izinsini uyembulile amazinyo, ukudala esibi vampire ngokumamatheka.

Olunye uphawu lesi sifo: amazinyo lihlehliselwe porphyrin, ngenxa yalesi sizathu, bangathenga umbala obomvu noma iba nsundu ngokubomvu. Isiguli sinelungelo kakhulu okhanyayo isikhumba ikhava. Esikhathini emini abazizwa ukucobeka eziqine futhi ukungabi namandla, amandla ebuyiselwa kuphela ebusuku. Kuyaphawuleka ukuthi wonke iqoqo izimpawu sici kuphela ngasekupheleni isifo esiteji. Zikhona nezinye ifomu ingasaphathwa abesabekayo porphyria.

Kwaze kwaba sengxenyeni kwekhulu lama-20 yesibili, Gunther isifo sasibhekwa njengophawu lokuthi cishe ezingelapheki. Kunobufakazi bokuthi e Ephakathi, ukuba lula isimo lesiguli wanikwa igazi fresh ubuyise bikho kwamangqamuzana egazi. Njengoba ungacabanga, lokhu akazange ukunikeza noma yimuphi imiphumela, ngoba isimo ngcono igazi, nje ukuphuza ingxenye yakhe, akunakwenzeka.

Iziguli porphyria akakwazi ukudla garlic, ngoba acid, ikhishwe le yemifino, inyuka okuholela ekulimaleni isifo. Izifo porphyria kungabangela okwenziwe usebenzisa ubuthi ezithile futhi amakhemikhali.