Goodpasture Syndrome: Ubangela, Izimpawu kanye Ukwelashwa Izindlela

Goodpasture Syndrome - ongavamile isifo sokuhlasela kwamasosha omzimba ukuthi kuhambisana isizukulwane omzimba atypical ukuthi ukuhlasela amaseli kwamaphaphu nezinso. isifo Okufanayo ogxile kuthinta amadoda abaneminyaka ephakathi kwengu-engu-12 no-35 ubudala. Kukholakala ukuthi iziguli abe propensity kwezakhi ukuphazamiseka ezinjalo.

Goodpasture Syndrome: izimbangela zezifo

Yiqiniso, isiguli komuntu yofuzo yilesi sifo. Noma kunjalo, kukhona izinto ezibanga ukusabela sokuhlasela kwamasosha omzimba.

With ukuthuthukiswa sifo izivikeli mzimba ukhiqiza amasosha omzimba ahlasela le ulwelwesi basal we-capillary ye-alveoli yamaphaphu kanye tubules kwezinso. Ngenxa yalokho yale nqubo kuthintwa waqhumuka capillary, okubangela ukopha zangaphakathi kanye nezimpawu ezihambisana.

Ngokokuqala ngqá leso sifo ilotshwe 1919. Kodwa kuze kube yilolu suku akwaziwa ukuthi icuphe ukuzivikela komzimba. Kukholakala ukuthi Goodpasture Syndrome lihlotshaniswa nezifo ezithathelwanayo. Ngezinye izikhathi ukusebenza kwawo Isifo esibangelwa amakhemikhali athile ubuthi. It ibhalwe ezimweni eziningana lapho lesi sifo basungula ngemva kokudla imithi.

Goodpasture Syndrome: izimpawu

Ngokuvamile, izimpawu zokuqala umgudu wokuphefumula. Isiguli ekhononda ka ubuhlungu besifuba, nokukhwehlela njalo futhi iphika ku ukuzikhandla. Ngokusho hemoptysis iqala nge ukuthuthukisa lesi sifo. Amaphaphu ungezwa kwesifuba ezimanzi noma ezomile. Isiguli bangase bakhathale njalo futhi ukozela. Ngezinye izikhathi kukhona okukhulu kwesisindo ngenxa ukwehla yemisipha. Ngokuphambene nalokho okukholelwa yiningi, ama-capillary emehlweni engabathinti sifo.

Njengoba kukhona okukhulu ukopha ezincane, izimpawu ezayo - kuba kwegazi, noma unenkinga yegazi eliphansi. Uma ulihlola isiguli, kungabonwa ukuthi isikhumba sakhe Uphaphathekile kakhulu. Kukhona cyanosis ka nolwelwesi lwamafinyila. Kwezinye izimo, ukuvuvukala kobuso ukuvela. Amazinga ngokuvamile lenyuka.

Izimpawu kwezifo izinso avele kancane kamuva. Ungase ukukhethwa esincane igazi umchamo uqaphela. ukwehluleka kwezinso ngokushesha futhi kuhambisana izimpawu lalo.

Goodpasture Syndrome: izindlela zokuxilonga

Ukuze lokwenza ukuxilongwa, udokotela kufanele uhlole ngokucophelela nesineke ukuze ubone imiphumela kanye ECG ukuhlolwa. Ngokuvamile, ukuhlaziya igazi kungabonwa yensimbi ukuntula anaemia , anda leukocyte ukubala, kukhuphuke ESR. Urinalysis kuthola umchamo e esiningi wamaprotheni ne amangqamuzana abomvu egazi. Kufanele nakanjani ukuphenya isikhwehlela, njengoba liyatholakala amangqamuzana abomvu egazi. Ingabe wusizo futhi spirography esisiza ukuthola ukwephula emishinini yokuphefumula zangaphandle. Nikeza futhi ECG cwaningo wegazi amagesi x-ray kanye biopsy ijwabu ezilimele, okuyinto wenza sikwazi ukubeka ukuxilongwa esichazayo.

Goodpasture Syndrome: Ukwelashwa

Eqinisweni, onalesi sifo ngoba iziguli enjalo okungekuhle. Futhi into ebaluleke kakhulu lapha - isikhathi ukuxilonga izifo futhi baqala ukwelashwa ngokushesha.

Ngeshwa, izidakamizwa ethize izifo ezifana ungekho. Kodwa kwazeke ukuthi ezimweni eziningi, ezanele umsebenzi yokwelapha syndrome luyaphela phakathi kwezinyanga 6-9. Uma ungayeka ukuthuthukiswa isifo so-renal kanye yamaphaphu, isiguli olungakwazi ukuphila khona. Ngokuvamile, odokotela linqume inani corticosteroids kokuthola. Plasmapheresis wenziwa, uma kunesidingo - ukumpontshelwa igazi , ngisho izinso ukufakelwa. Ukuze uyeke ukuthuthukiswa igazi nensimbi ukuntula yokugcwalisa anikeze isiguli imithi ezifanele. Kodwa ngezinye izikhathi, futhi ezimweni ezinzima kakhulu, ukumpontshelwa igazi liyadingeka zokuqeda igazi.