Etiology ka sarcoidosis nalokho izifo udidekile sifo Lefgrena

Lefgrena syndrome - a ziyalingana ISIZINDA hilar bronchopulmonary uhlelo lymph nhlangothi zombili. Izifo ephelezelwa isikhumba ukubonakaliswa (erythema nodosum), imfiva, futhi arthralgia. Lezi izimpawu nobuntu sarcoidosis.

Lapho lesi sifo sihlasela izitho ezahlukene - emaphashini, ubende, izindlala zamanzi. Lefgrena syndrome sarcoidosis ayihambi futhi akuyona esithathelwanayo. Hhayi ukuze kudidaniswe oncologic isifo izinqubo kanye nesifo sofuba.

emitholampilo isithombe

Sarcoidosis bekulokhu Adalberto isikhathi eside isifo ezingavamile, kodwa namuhla isimo sesishintshile, zokugula zibhebhetheka ngesilinganiso okusheshayo emhlabeni wonke. Ngokwezibalo, ngaphezu kwanoma ubani omunye ebhekana syndrome Lefgrena abesifazane abaneminyaka engu-20 kuya kwengu-40, kodwa isifo ongeza muntu.

Kungenzeka ngaphandle izimpawu kancane noma ngendlela oyingozi. umtholampilo Asymptomatic ngokuvamile ukutholwa ithuba zokuvimbela fluorography luhlolo. Okuvame kakhulu kuyinto inchubekelembili kancane kancane lesi sifo futhi i-izimpawu ezilandelayo:

• dyspnea ku ukuzikhandla;
• ubuhlungu buthuntu esifubeni;
• ubuhlungu phakathi izindwani ehlombe ;
• isifuba esomile lapho;
• ongaphakeme-ebangeni imfiva ;
• ukukhathala noma ukuba buthakathaka;
• ukujuluka ngokweqile;
• ukungakuthandi ukudla;
• ubuhlungu bamalunga emhlane ephansi.

Ahlekise sarcoidosis ngokuthi syndrome Lefgrena, kuhambisana ngokuvusa lokushisa ukuze 38-39 ° C, ukuqaqamba kwamalunga omzimba, izilonda zesikhumba ngesimo erythema, ubuhlungu besifuba kanye iphika. Akuyona into engavamile e-acute ngesikhathi alulame ngokugcwele ngaphandle kokusebenzisa imithi yokwelashwa komuntu kanye nalokunye kungenelela.

Etiology lesi sifo

Kuze kube sekupheleni izimbangela imithi eyaziwa yalesi sifo, kungenzeka ukuthi kumkhathaze ngokuhlela lezi zinto ezilandelayo zingase ukuthuthukisa:

• ukutheleleka, Mycobacterium sofuba, i-hepatitis C;
• iziphi izici zangaphandle ezingezinhle, ukuhogela uthuli insimbi;
• ukubhema, engesiyo imbangela, kodwa kakhulu inkimbinkimbi inkambo isifo;
• ufuzo.

Ukuvimbela sarcoidosis

Abagulayo syndrome Lefgrena ezibalulekile ukuyeka ukubhema, ukusheshisa yokutakula. isikhathi Kuyadingeka yini sizihlole izinhlaka esifubeni eminyakeni 2. Ikhumbula yokuthi etiology lesi sifo akwaziwa kuze kube sekupheleni, izimiso of izinyathelo zokunqanda ukuba athuthukiswe. Ochwepheshe batusa ukuba sizigweme uthuli zensimbi foci ukutheleleka.

Lefgrena sarcoidosis syndrome Kutholwe elandelayo extrapulmonary kwasendaweni inqubo - ukunqoba nezicubu ongama, isikhumba kanye neuropathy zamanzi. Kukhona ukwanda wesibeletho, subclavian, axillary futhi ISIZINDA inguinal. Kwezinye izimo, le abathintekayo lymph node esiswini.

Bone futhi uqondiswe isimiso sezinzwa esiyinhloko iyathinteka ingasaphathwa njalo, kodwa kunzima ngoba lesi sifo zenzeke. Sarcoidosis wenhliziyo kwenzeka 20-30% of amacala kukhona asymptomatic. lwesokunxele inhliziyo ziyancipha emqulwini, ilungelo ventricle iyakhula.

luhlolo nasekwelashweni inikezwe amathuba uthembele umphumela omuhle. Kwelinye icala, zikhona izinguquko wamaphaphu izicubu, eyagcina kuholela ukukhubazeka.

Lefgrena syndrome sarcoidosis acute samuntu

Ngokuvamile kudidaniswe sarcoidosis, isifo sofuba ngenxa yokufana izimpawu. Lokhu kudinga ukuxilongwa okujuli-, ngoba izimbangela kanye therapy ezahlukene. Akunakusetshenziswa asikwazi wahlanganyela self-ukwelashwa, ikakhulukazi ukuthatha imithi senzelwe iziguli ngesifo sofuba, kungaholela ekufeni.

Lefgrena syndrome (isibonelo zakudala) - lokhu lapho isimo jikelele isiguli wocwanigo egculisayo. Kunezinguquko esikhumbeni. Kwangathi avele:

• papules futhi zingcwecwe;
• Chilblains lupus;
• izibazi keloid;
• lingene;
• erythema nodosum;
• SKD futhi CKD sarcoid Beck;
• ISIZINDA amaningi obukhulu kule izicubu ongama.

ukuhlola

Ukuhlolwa iziguli Lefgrena syndrome ukwenza-X-ray. Njengoba indlela intuthuko usebenzisa computed tomography. Ukwenza kwamakhemikhali kanye segazi.

Inkinga kwelashwa ukucindezela ukuvuvukala. Indlela esebenza kahle kakhulu ukusetshenziswa corticosteroids izinyanga eziyisithupha. Uma sithinta izitho ezibalulekile liyadingeka glucocorticosteroid yokwelapha i-hormone.

Ngokushesha Yiqiniso okuqhubekayo ziphathwe amafishane yokuphathwa emthanjeni izidakamizwa eqeda ukuvuvukala. Ezimweni lapho ukwelashwa akanamandla, aphethwe plasmapheresis (igazi uhlanzekile). Ngesikhathi ezinzima wamaphaphu esiteji isifo zidinga Ukufakelwa izitho zezinzwa. Inkambo weni nasekwelapheni tifo umphumela kakhulu evumayo, kodwa akudingekile ukuba uqale inqubo.