ImpiloIzifo nemibandela

Syndrome elongate slot qt: incazelo, izimbangela kanye nokwelashwa izici

Human Health - ingxenye eyinhloko ezejwayelekile kanye izinga lokuphila. Kodwa asizizwa okunempilo njalo. Izinkinga zingase ziphakame ngenxa yezizathu ezihlukahlukene, futhi ukubaluleka kwabo nakho kungaba ezahlukene. Ngokwesibonelo, umkhuhlane akakubangeli izimfuno zabantu, ke welashelwa ngokushesha futhi akakubangeli umonakalo omkhulu kakhulu kwezempilo jikelele. Kodwa uma kuphakama izinkinga zangaphakathi, kuyingozi esengeziwe ukuphila futhi unomphela olimaza enhlalakahleni yethu.

Muva nje, abantu abaningi ukukhononda izinkinga zenhliziyo avame kuba izifo ezivamile kulula ukwelapha nokuxilonga. Kodwa zikhona izikhathi lapho isiguli itholwa eside syndrome qt. Kwezokwelapha, leli gama kuyinto Isisho noma isimo atholwe lomuntu, ephelezelwa ukwanda ubude ECG ingxenye isikhawu. Futhi yilesi sifo kuthiwa kubangelwa ukunwebeka kuphela ms ezingaphezu kuka-55 kusukela amagugu evamile. Kulokhu-ke lapho isifo eba, indices sokusuka we isikhawu ingase ingabi 440 ms.

ukubonakaliswa

Ezimweni eziningi, isifo lesiguli kuyinto asymptomatic nokuzihlonipha, ngokuba nezingxabano ukuthola cishe akunakwenzeka. Ngokuvamile, abantu nale Ihlahlubo i- repolarization futhi depolarization ngenxa yezinguquko ziyalingana innervation zenhliziyo. Isaziso kungenzeka kuphela ngokuhamba nophenyo, ngesisekelo imishini ezihlukahlukene. Isici esiyinhloko ukuba nengxenye kule simo ukuntengantenga kagesi imisipha yenhliziyo.

Abantu abangenawo elongate slot qt syndrome ekwelashweni ayizwakali noma ukungezwakali kwawo ingaqala ventricular fibrillation noma ventricular tachycardia. Lezi zinkinga eziyingozi kakhulu ngaphezu izimpilo zeziguli, sithwale bangakunaki isimo jikelele. Ngakho-ke, uma usola khona lesi sifo kufanele ngokushesha unakekele impilo yakho, uma kungenjalo ungase nemiphumela emibi. Ngaphezu kwalokho, ngenxa yezinkinga lesi sifo sina ngempela. Abakwazi nje kuholele ukungasebenzi kanye Ukuwohloka isimo lesiguli jikelele impilo, kodwa futhi ebulalayo.

izinhlobo

Kwezokwelapha Sekuyisikhathi eside ke wafunda ukuphambuka enjalo, futhi phakathi neminyaka edlule ososayensi uphathe afunde okuthile ngako ngaphezulu. Lesi sifo ihlukaniswe izinhlobo ezimbili ezibaluleke kakhulu, okuwukuthi, usezuze futhi azalwa naso eside qt syndrome isikhawu. Nquma ukuthi iyiphi uhlobo nesineke, can indlela ucwaningo kuphela. Lapho iziyaluyalu azalwa naso inkinga ukwehluleka isimiso sezakhi zofuzo. Lapho uthenga ekuthuthukiseni lesi sifo okuthintekayo izici ezihlukahlukene.

ukuma

Futhi secrete ezithile zalesi sifo:

  • ifomu esicashile. It libhekene izinkomba evamile isikhawu phakathi luhlolo, nokuhlasela lokuqala nakwisyncope kuyinto ngokufa okuzumayo.
  • izikhathi zokufika ka nakwisyncope, kodwa QT isikhawu akuyona enwetshiwe ngesikhathi sokuhlolwa.
  • Ukunwebeka isehlane isikhawu futhi is hhayi kubonakala emlandweni.
  • Syncope zenzeka ne ukunwebeka Inkomba qt, beyizidlova ngesilinganiso 440 ms nangaphezulu.

izizathu

Ziningi izici kungathikameza ukukhula yalesi sifo. Isibonelo, ucala kutfutfukisa yizifo lezinceku kuhlanganise syndrome P-U. Kulokhu ngokuvamile kakhulu lo nokulahlekelwa ukwazi nokuquleka ukuthi empeleni kungaholela ekwakhiweni kwalesi sifo. Futhi, E-P-A syndrome, uma isiguli sine-ubuthulu azalwa nako. Siyini isizathu inhlanganisela enjalo izimpawu futhi icuphe kanjani ukuthuthukiswa lesi sifo, ososayensi bathola izinto ngaphandle kuze kube manje kuhlulekile. Futhi, isakhi sofuzo kuguquka kungabangela ukuthuthukiswa lesi sifo. Lokhu kuyimbangela eyinhloko yesifo azalwa naso, kodwa kwezinye izimo akusiyo ngokushesha, futhi njengoba omdala, ngemuva kokuxinwa ukucindezeleka. Ngokuvamile kuba inkinga zamagama amaprotheni sodium ne-potassium zeziteshi izici ukuthi kumkhathaze elongate qt isikhawu syndrome. Isizathu angase alale ku Imiphumela emibi yemithi ethile. usongo Iningi kukhona imithi elwa namagciwane eqinile ukuthi isiguli kungathatha ukwelapha ezinye izifo.

Kungabangela isifo noma Ukudla umzimba ukunciphisa kilojoule ukudla. Ukuncipha kwamanzi angaphansi umzimba kulezi zimo kungenziwa kubonakala nje kuphela inhliziyo. Ngakho-ke, ukudla okunjalo kungcono ukuxoxa nodokotela kanye igcinwe ngaphansi kweso lakhe. Ukuzithumela kwezinye izindawo nokufa kungaholela yezinkinga ezinye izifo zenhliziyo ezifana senhliziyo noma mitral valve prolapse. ngezinye izikhathi syndrome ngenxa CNS pathologies kanye dystonia semithambo kanye nezinye izifo autonomic nesimiso sezinzwa.

izimpawu

Zikhona izimpawu ezithile ezibonisa ukuthi isiguli samanje qt eside syndrome. Izimpawu zalesi sifo zihlanganisa:

  • Nokulahlekelwa ukwazi ihlale imizuzu embalwa a ngekota yehora. Kwezinye izimo, kuba khona okuhlaselayo kungathatha amaminithi amabili.
  • Ngibanjwe e izimo anokulandisa okufanayo like isithuthwane ngokubukeka, kodwa izinqubo ezibanga kubo awafani.
  • ubuthakathaka okungazelelwe umzimba, ephelezelwa ukuhwalala samehlo.
  • Palpitations ngisho nalapho engekho womsebenzi ukukhandleka noma ukucindezeleka ngokomzwelo.
  • Chest ubuhlungu bemvelo ezahlukene, waqhubeka kanjalo phakathi kwenhliziyo okusheshayo, kanye lokuhamba nabo niphele amandla noma isiyezi kanye ndikindiki ezandleni nasezinyaweni.

ukuhlola

Isikhathi esining impela, eside syndrome qt, ezinganeni ikakhulukazi, asinazo izimpawu. Kulesi simo, isiguli singase uzizwa uphile kahle ngokuphelele futhi efa ngokuzumayo. Ngakho-ke, uma umuntu isengozini lesi sifo, kufanele njalo uhlolwa udokotela wokuthi yadalwa ukuthi kungenzeka ukuthuthukisa lesi sifo. Ukuxilonga izifo, ezokwelapha zesimanje isebenzisa izindlela eziningana.

Uma kukhona izinsolo ukuthi isiguli futhi eside qt izinkinga syndrome impilo abonisa ngokucacile lokhu, le electrocardiogram - isifundo esibaluleke kakhulu ukuthi kubonisa isifo. Ngaye ngesikhathi kuhlasela, iyunithi sizobonisa izimpawu tachycardia ventricular, wedlula ku ventricular fibrillation. Le ndlela kuyinto eyinhloko lesi sifo ngesikhathi kuthathwa isinqumo.

Kukhona esinye isifundo ukuthi wembula side isikhawu syndrome qt. It wenziwa emini. Ngakho, ubizwa ngokuthi ukuqapha ECG. Lolu cwaningo ivumela ukulungisa umsebenzi lesiguli inhliziyo ngalesi sikhathi. Ukuze umzimba ninamathele kudivayisi yakhe encane ukuqopha ubufakazi inhliziyo, futhi ngemva kususwe, uchwepheshe wahlanganyela efunda okwakubhalwe kulowo mbhalo iqoshwe idivayisi idatha. Bavumela ukuba inqume ukuthi isiguli bradycardia ezinzima eqinile ngabe izinguquko morphology T igagasi, kanye ngabe kukhona kungukuphula izinqubo repolarization esivimba amanzi futhi ventricular amabhithi kwesikhathi.

ukwelashwa

Uma isiguli sekutholakale qt eside syndrome, ukwelashwa kufanele kube olunzulu futhi kufaneleka, ngoba indlela kuphela ukuvimbela ukuthuthukiswa yezinkinga eziyingozi empilweni kanye ingakwazi ukuthwala umphumela obulalayo.

ukwelashwa

Lesi sifo ingelapheka usebenzisa izidakamizwa antiarrhythmic. Yiqiniso wezokwelapha akhethwe kahle ngeke aqede kuphela izimpawu zalesi sifo, kodwa futhi kuze kudlule isikhathi eside ngaphambi kokuba izinze yisimiso senhliziyo nemithambo yegazi. Lena ngenye yezindlela ukuze elashwe syndrome azalwa naso we isikhawu side qt LQTS.

ukwelashwa kuhlinzwa

Uma isiguli sine-engozini ekuphileni ngenxa arrhythmias kule isifo, ochwepheshe batusa ekugxiliseni elingenalo iwashi lenhliziyo. umsebenzi wakhe kujwayeleke ukuvama Kufinyeta of imisipha yenhliziyo. imithi yesimanje uye wazakhela idivayisi ekhethekile, enquma ukuphambuka sokugembula zenhliziyo. Ukugula kungadalwa kusuka ngaphandle. Phakathi umsebenzi, isibonelo, idivayisi ngeke aphendule. Kodwa uma pulses uzobe iletha yi umlingisi sokugembula, ke normalizes umsebenzi umzimba.

Umsebenzi at isifo ezifana side qt syndrome isikhawu, elula futhi ephephile ngokwanele. Pacemaker eqondiswa kwesokunxele pectoralis kwemisipha emikhulu. Kusukela kulo bangabantu electrode ukuthi odokotela kuvikelwe endaweni oyifunayo, ubaqondisa ngokusebenzisa vein subclavian. I-apharathasi kungase kushintshwe ngu uMklami. Nayo ungakwazi ukushintsha kwemigomo ukukhuthazwa inhliziyo, kuncike izici siqu isiguli. Powering kuzokwenzeka njalo uma umsebenzi imisipha yenhliziyo ziyoba ngaphezu kwalokho nemingcele ebekiwe.

isiphetho

Lesi sifo ngaso sonke isikhathi ukuthi ukuxilonga ngoba kuyaqabukela Inkulumo kubonakala. Kodwa ngesikhathi esifanayo usongo lwezempilo lesiguli likhulu kakhulu. Ngakho-ke, uma kukhona ngisho ingozi kancane lapho ivela khona, kufanele ubanjwe njalo ucwaningo bese uthintane ochwepheshe. Uma uphethwe kuqinisekisiwe, kumele kube impatho oluphelele futhi ephelele yalesi sifo, ngoba kungaholela ekufeni.

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