Myasthenia Gravis: izimpawu, uphethwe, ukuphathwa

Namuhla, ziningi izifo sokuhlasela kwamasosha omzimba. Omunye kungaba ukuqeda ngosizo yokwelapha abakhethiwe kahle, kuyilapho abanye bengasabeli lokwelashwa, futhi into nje abazokwazi imithi - ukuvimbela exacerbations.

Lesi sihloko Bayokhuluma izifo ezifana myasthenia gravis: izimpawu, uphethwe nasekwelashweni kwezifo kungakephuzi - zonke lezi zikhathi izozama ukuxoxisana ngokugcwele ngangokunokwenzeka. Ngaphezu kwalokho, thola cishile bani uchayeke kakhulu izifo, kunezindlela ukuzigwema enjalo lapho.

Kuyini myasthenia gravis?

Myasthenia gravis kuyinto isifo sokuhlasela kwamasosha omzimba esibangela okuqhubekayo buthakathaka kwezicubu. Lokhu kwenzeka ngenxa ukwehluleka ukudluliswa kwamanyuroni. Ezimweni eziningi, imisipha ethintekile amehlo, izinsini ubuso, okungenani - kokwenza umsebenzi zokuphefumula.

Njengoba izibalo zibonisa, myasthenia gravis ivame abesifazane abaneminyaka ephakathi, nakuba eminyakeni yamuva uqale ukulotshwa nje isizukulwane esisha.

Ukwahlukaniswa izifo

Cishe zonke isifo kungenziwa labizwa ngohlobo. Ngineminyaka engu azihlukile futhi myasthenia gravis. Ifomu lesi sifo kungase kuxhomeke ezicini eziningana, ngakho-ke, sibheka lwezinhlobo ezivame kakhulu.

Kuye iqembu yobudala myasthenia nesineke gravis kungaba:

• azalwa naso;
• izinsana;
• inkinobho yesinxele segundane
• abadala;
• version kamuva.

Kuye izimpawu zokwelapha lesi sifo yilezi ezilandelayo izinhlobo ngokuthi myasthenia gravis:

• umumo iso;
• zemisipha;
• pharyngeal nobuso;
• generalized.

Izimpawu ngayinye izinhlobo zesifo sichaziwe ngezansi.

Izimbangela zesifo

Imbangela sifo namanje uhlala yayingaziwa nhlobo. It is kuphela eyaziwa ukuthi isifo kwenzeka ngenxa ukuvaleka omzimba zemizwa imisipha. Ngenxa yalokho, awakwazi ukuphendula lo kuphumele amasignali kwemizwa.

Lesi sifo myasthenia gravis kungaba azalwa naso noma bathenga. Ifomu yokuqala lingandile kangako, nezimbangela zayo kukhona ukuguquka kwezakhi zofuzo.

myasthenia Kutholiwe gravis kungaba ukuzibonakalisa phezu thymomegaly isizinda (ingozi Hyperplasia Prostatic, thymus) noma izimila. Ngaphansi ngokuvamile, imbangela isifo kungaba isifo sokuhlasela kwamasosha omzimba, njenge-scleroderma noma dermatomyositis.

Kukhona Ezimweni eziningi lapho myasthenia gravis athuthukile ngokumelene isizinda umdlavuza. Ikakhulukazi, kumayelana isimila izitho zangasese (wendlala yabesilisa, esibelethweni), okungenani - isibindi, iphaphu, nokunye.

izimpawu

Yini izimpawu kuzosiza lokwenza ukuxilongwa, "myasthenia gravis"? Izimpawu zingase zihluke noma kuhlanganiswe kuye ifomu nesigaba lesi sifo.

myasthenia Ocular gravis kuthinta:

• imisipha isiyingi esweni;
• imisipha iso ;
• imisipha, okuyinto unomthwalo oqeda leso elingenhla.

Ngenxa yalokho, izimpawu zalesi uhlobo lesi sifo kungase kube kanje:

• nobunzima ngokugxila emehlweni;
• strabismus;
• umbono double;
• nakwenzeka isikhathi eside ukubheka izinto ezikude noma eseduze kakhulu;
• alengayo leso elingenhla (ptosis).

Lokugcina izimpawu kubhekwe kungaba ukuzibonakalisa kuphela kusihlwa futhi ekuseni engekho ngokuphelele.

ifomu phambi myasthenia gravis ephelezelwa zimpawu:

• ushintsho izwi, okuyinto iba "impumulo" nezimpumputhe;
• nobunzima ngenkulumo (isiguli uyakhathala ngisho emva kwamaminithi ambalwa yengxoxo);
• nezinkinga ukudla (isiguli kunzima kakhulu ukuhlafuna ukudla okuqinile ngenxa yobuthakathaka imisipha okuhambisanayo).

Lapho kunqotshwa we pharynx kukhona awokuthi amanzi ingress phakathi ipheshana zokuphefumula. Lokhu kungenxa yokuthi isiguli sikwazi ukuthatha ukudla okuqinile futhi angaminyanisa, okuyinto kwenzeka kaningi impela. Ngenxa yalokho, igcwele ukuthuthukiswa nenshisekelo nenyumoniya.

ifomu zemisipha lesi sifo kuhambisana ukukhathala ingxenye ethile yomzimba. Ezimweni eziningi, lokhu kusebenza nasemilenzeni. Kukhona amacala lapho isiguli singenakukwazi ngisho ukuthatha indebe evamile yamanzi noma ukukhuphuka izitebhisi.

I esiyingozi kakhulu kuyindlela generalized lesi sifo. Kubonisa nobuthakathaka imisipha yokuphefumula, okungase kuholele hypoxia oyingozi futhi ukufa.

Njengoba ubona, myasthenia gravis, izimpawu zazo zahlukahlukene kakhulu, kuyinto izifo sibi kakhulu futhi ezisongela ukuphila. Yingakho-ke kubalulekile ukuba uqaphele ukuvela inkinga futhi ukuthatha amanyathelo wonke afaneleyo.

Ngakho-ke, izinto ezilandelayo okuzoxoxwa kohlaka ngesihloko esithi "Myasthenia Gravis", - ukuxilongwa nokwelashwa kwezifo kungakephuzi.

isevisi kuyinto

Myasthenia Gravis - lena ngempela isifo ezingavamile. Ngakho-ke, udokotela wezinzwa abanakwethenjwa ngaso sonke isikhathi okusheshayo ukwenza ithole ukuxilongwa okufanele.

Yini okufanele yenziwe ukuba bakwazi ukubona izifo yezokwelapha ezifana myasthenia gravis? Sifo kungabandakanya:

• ucwaningo nesiguli khona izikhalazo;
• luhlolo emitholampilo;
• prozerinovoy beqhuba izivivinyo;
• Ukuhlolwa nge edrophonium;
• cwaningo electromyographic;
• sokunquma ezingeni amasosha acetylcholine zemizwa serum;
• iso ukuhlolwa;
• computed tomography kwesifuba;
• MRI;
• hlola wamaphaphu function.

Phakathi nesifundo, kubalulekile ukuqeda zonke izifo kunokwenzeka, izimpawu zazo ngezinga elithile efana izimpawu myasthenia gravis. Ngokwesibonelo, kungase kube syndrome bulbar, Izifo ukuvuvukala (meningitis, encephalitis), isimila kumiswa ku brainstem (hemangioblastoma, glioma), isifo Neuro-kwemisipha (myopathy, Guillain, ALS, njll), i-cerebral ukugeleza kwegazi (instult ischemic ) nokunye.

imithi ye myasthenia gravis

Kuye ngezimpawu, futhi nesigaba lesi sifo ziyahlukahluka nohlobo yokwelapha.

Le nqubo kuqala kudinga izidakamizwa ukuthi ngcono ukudluliswa ngiyibona at kokuhlangana kwamanyuroni. Ngokuvamile asetshenziselwe le nhloso ezifana ejenti kwemithi ngokuthi "oksazil", "Neostigmine" "Pyridostigmine" nokunye. zonke zibe uhlobo olufanayo isinyathelo futhi ukwandisa lokuhlushwa acetylcholine. Le mithi kukhona impela ukususa lesi sifo kusaqalwa sokuthuthuka, kanye ngesikhathi kuqala ezihluzekile ngesikhathi sezinhlekelele.

Into elandelayo okudingeka uyenze - ilungelo ulungise amanzi electrolyte ibhalansi emzimbeni. Lokhu kuzodinga eyanele has B amavithamini kanye potassium ukuqinisekisa umzimba evamile.

Ukuqhubeka kwesifo kuhilela ukwamukelwa of nolaka izinyathelo ukwelashwa. Zakhiwa e reception hormone immunosuppressive. Naphezu kweqiniso lokuthi le mithi kabi ikubekezelele umzimba, kuzuze ukusebenzisa kwabo okukhulu ezingaba engemihle, ikakhulukazi uma kuziwa ekulondolozeni impilo hhayi kuphela, kodwa futhi ekuphileni.

Nakani!

Kukhona ezinye izidakamizwa ukuthi basuke nhlobo ukwenza uphethwe "myasthenia gravis". Lezi zihlanganisa i-beta-blocker, magnesium nosawoti, calcium abamelene, imithi elwa namagciwane, aminoglycosides, ama-hormone egilo, zinhlungu, morphine, i-quinine-derivatives, antipsychotics, barbiturates, futhi hypnotics kakhulu futhi sedatives.

Ngaphezu kwalokho, kumelwe singakhohlwa ukuthi iyiphi ikhambi elenziwa zingafundwa kuphela ngemva kudokotela, ikhumbula zonke izici ngamunye umzimba.

Ukwelashwa nge ukuhlinzwa

ukwelashwa akusho ngaso sonke isikhathi alethe nemiphumela ayeyifuna, futhi ukuqeda le nkinga. Ngakho-ke, ngokuvamile kuyadingeka ukuze kokungenela kuhlinzwa. It yena, kungafaka ebambe eyodwa noma izinqubo eziningana:

• ukupholisa mechanical uma nakwenzeka ukuphefumula nokuguqulwa;
• plasmapheresis igazi purifier omzimba normal, lapho inqubo kumele kwenziwe njalo ngezikhawu ezithile;
• occupational therapy kanye Physiotherapy - lezi izinqubo ezimbili awawaqedi lesi sifo, kodwa ungakwazi ukusiza isiguli ukuba sibhekane ngokuphumelelayo ekushintshashintsheni amandla kwemisipha.

Ngaphezu kwalokho, kungase kudingeke ukuba asuse le ndlala thymus ngokusebenzisa ukuhlinzwa.

Isiqu yokwelapha cell

Lolu hlobo ukususa inkinga ongakabi eyathandwa kakhulu, kodwa noma kunjalo kuwufanele ukukhumbula futhi ngaye.

Ukwelashwa nge-stem cell ethathwe izicubu adipose, luveza okusezingeni eliphezulu kahle ngokwanele ekulweni nesifo. Isiza isandiso esiphezulu kwenkathi ukuthethelelwa. Healthy stem cells ukusiza ukulungisa izinqubo ukuphefumula nokugwinya. Ngaphezu kwalokho, bathuthukisa nokuqedwa ptosis e esikhathini esifishane.

Inkambo yokwelashwa kanye nokuvama nokuphathwa stem cells emzimbeni kungaba kuphela nika Uchwepheshe abanolwazi!

Hlahluba okuzayo

Ngisho nangekhulu elidlule, sitholakele "Myasthenia 'wayesho ngoba wayebona ukuthi usezokufa. Kodwa isikhathi sihamba, futhi imithi akemi namanje. Okwamanje, sisungule ezihlukahlukene imikhiqizo ekhethekile siyosiza ekusindiseni izimpilo, wandise inkathi ukuthethelelwa.

Ngesikhathi esifanayo kumelwe singakhohlwa ukuthi gravis myasthenia kuyinto isifo esingelapheki. Lokhu kusho ukuthi iziguli kuyodingeka sonke isikhathi ukuba ukuphathwa (noma amazinga njalo) ukuze ulondoloze impilo. Akunzima ukuqagela ukuthi izinga lokuphila kuleli cala bangase kakhulu ahlupheke.

Ngakho-ke kuyadingeka egcizelela ukuthi kuphela ukuxilongwa esifike ngesikhathi lesi sifo ungayeka inchubekelembili yayo ngendlela esifike ngesikhathi futhi ligweme izinkinga ezingase zivele.

zokuvimbela lokubuya kwesifo

Saxoxa ngale zokugula njengoba myasthenia gravis. Kuyini, lokho kuhambisana ngezimpawu zesifo nokuthi kukhona ukwelashwa okuphumelelayo lesi sifo, kuyaxoxwa. Ekugcineni ngingathanda ukuba zihlale kubo nezindlela zokugwema ngiwela ogibeni lwezidakamizwa, njengoba for iziguli, isihloko sihambisana kakhulu.

Okokuqala, isitatimende ezibalulekile kwi-akhawunti wezinzwa. Kulokhu, kunoma yiliphi icala ungaphuthelwa amathekhiniki kuhlelwe, kodwa uma kwenzeka izimpawu kufanele uxhumane nodokotela elwa, hhayi elinde ekuhambeleni okulandelayo.

Okwesibili, kubalulekile ukuba ubuyekeze futhi, uma kunesidingo, ulungise impilo yakho evamile. Iziguli myasthenia akukho izimo kufanele khona ukukhathala ngokomzimba, ngakho-ke kuhle ukukhetha umsebenzi, ukuhlinzeka umsebenzi ngokwengqondo. Uma kungenzeka, kufanele nomkhawulo isikhathi uhambo, ikakhulukazi maqondana ezokuthutha zomphakathi.

Akufanele sibakhohlwe ukuthi yisiphi isifo, ngisho SARS, kubangela ukucindezeleka komzimba kanye ukuphazamiseka kwesimiso somzimba sokuzivikela ezifweni. Ngakho-ke kubalulekile eduze nokuqapha isimo sempilo yabo, ukuvimbela hypothermia hhayi ukuba ezindaweni ne lokuhlala ezinkulu zabantu esikhathini yokudlanga jikelele yezifo ezithathelwanayo.

Ephambi kwezinduna myasthenia gravis othola imithi kufanele kuvunyelwane nodokotela wakho, ngoba kukhona Izimo eziningi ezikhethekile (abanye bakhumbula nga phezulu them).

Ingabe akazibekanga medicate futhi ube nempilo!