Impilo, Izifo nemibandela
Muscat isibindi: anatomy, Histology, patomorfologija
Muscat isibindi - phetho ezingamahlalakhona congestive plethora emithambo yegazi yezitho zangaphakathi. Lesi simo sibonakala hhayi kuphela isimiso sokugaya ukudla bungene, kodwa inhliziyo, amaphaphu, izinso kanye nobuchopho.
ngezigaba
- Muscat isibindi: ku isizinda okunamafutha amaseli (ophuzi) kubonakala vasodilatation (obomvu amnyama).
- cystic Emgodini onomthombo: indwangu kuyinto ayazika ngenxa ezicutshini of ukuhluma. Igazi soaks le parenchyma isitho, kanye kokuvela izilonda sclerosis.
- Senhliziyo isifo sokusha: surface body iba ukubukeka engalingani.
omsakazo
Ukwephula ukugeleza kwegazi emiphumeleni uhlelo portal kwetinhlavu ezinjengokungcoliswa Muscat isibindi. Izimbangela yokujama tsi - kuphula umthetho we ventricular umsebenzi kanye nokuncipha ukubuya emithambo yegazi. Lokhu okubonakalisa congestive ukumelwa inhliziyo, futhi zivame ukuhambisana nesifo senhliziyo nemithambo yayo. ingcindezi Ukwandisa uhlelo emithambo yegazi, kanye ukucinana yokujama tsi igazi imithambo yegazi zithikameze ngempumelelo ukugeleza kwegazi kwezitho zomzimba.
lwezifo
engcupheni isifo sesibindi kukhona ukungawuvivinyi umzimba, ukudla okungenamsoco, imikhuba emibi, khona isifo senhliziyo emlandweni, kanye yobudala umuntu omdala sika.
umtholampilo
ukuhlola
1. Ukuqinisekisa ubukhona yinhliziyo (instrumentally noma behlolwa):
- -X-ray yesifuba (ekhombisa ukuguquka kwenhliziyo, ukuminyana emithambo yegazi emaphashini, noma ukuba khona effusion pleural);
- Doppler Ukuhlola inhliziyo, futhi bakhiphe elezinga eliphansi vena cava (ukuhlonza izimbangela yesifo senhliziyo);
- CT noma i-MRI;
- ECG.
2. Feza ukuhlolwa laboratory yegazi, njenge-chemistry kokusebenza kwesibindi ukuhlolwa :
- igazi bilirubin owandiswayo;
- transaminase ngokulinganisela anda (ALT, AST);
- nesanda phosphatase ane-alikhali;
- wehlise e-albumin futhi ayewukela isikhathi ekunqandeni.
3. Baphendukele ukuhlola wezinsimbi, ukusungula iqiniso ukonakala morphologically kwesibindi. Lezi izifundo zihlanganisa:
- laparocentesis (khulula aspirating uketshezi ngaphakathi komgodi ongaphakathi kwamathumbu) ukunquma izimbangela ascites;
- biopsy inaliti (ukuqinisekisa ukuxilongwa "Muscat isibindi" amaslayidi zingenziwa futhi ukuphila lesiguli).
Imiphumela yaloku kuhlola okungenhla Comparative kuhlanganisa izifo ezifana isifo sokusha oludakayo, umdlavuza, isifo senhliziyo, hemochromatosis, thrombosis ka bakhiphe elezinga eliphansi vena cava kanye nomfutho wegazi ophezulu portal. Ungakhohlwa mayelana izifo ezibangelwa amagciwane isibindi - nokohlobo A, B, C, D, E. Ngaphezu kwalokho, kukhona kungenzeka isifo yisinanakazana.
yezinkinga
ukwelashwa
ukwelashwa kufanele okuhloswe ngalo ukubhekana nesifo ecashile, okusho yokumelwa yinhliziyo. A isifo sokusha ngokwako ayinakho oluthile lokwelapha. Ngaphezu kwalokho, isiguli uyayalwa ukulandela ukudla nge izivimbelo usawoti isifuba ukushintsha oda usuku lwakho ukulala kahle, abe ngaphandle futhi ukuvocavoca umzimba ngokwanele. Lezi manipulations elula kungasiza ukunciphisa umfutho wegazi izitsha ezinkulu, kuhlanganise e vein portal.
therapy okunezimpawu kuyinto isisu (ukunciphisa inani loketshezi esiswini), ne-beta-blocker futhi ACE inhibitors (i-ukuzinza wenhliziyo).
ukwelashwa Steel ngokuvamile hhayi lwenziwa. Lihlobene nokubhekana ubuso nengozi enkulu ukuze isiguli futhi akusho bathethelele uqobo. Ngezinye izikhathi, udokotela angase anqume ukundlula ingxenye vein portal intrahepatic, kodwa lokhu kungaholela ezinzima inhliziyo ukwehluleka ilungelo uhlobo ventricular futhi edema yamaphaphu ngenxa ngokucijile ukwandisa ukubuya emithambo yegazi.
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