Gilbert Syndrome: kuyini? Izimbangela, izimpawu kanye nokwelashwa isifo

Lesi sifo kuhambisana ukuphazamiseka bilirubin umzimba, saqale ezichazwe 1901 by A. N. Gilbert (Gilbert). Ngokwezibalo, ne isifo esifanayo ubhekene mayelana 5-7% labantu emhlabeni. Ngakho kungani kukhona Gilbert Syndrome, kuyini futhi yiziphi izimpawu zaso? Ingabe kungenzeka ukwelapha ngokuphelele lesi sifo?

Gilbert Syndrome: kuyini?

Ukuze uzwisise kahle lesi sifo yilokhu ngenxa, kubalulekile kuqala ukuthola ezinye izici bilirubin umzimba. Lokhu sombala ophuzi, kwakheka okuyinto esibindini ngu ukubola-hemoglobin (lo mbala zokuphefumula wegazi). It is ibe mahhala ophuzi sombala ifomu eboshiwe izicubu isibindi. bilirubin okunjalo conjugated iwela gallbladder, bese kuqhutshekwa kanye Bile ku ipheshana wokugaya ukudla bese excreted ne indle. Lapho lesi sifo bilirubin olukhululekile ku inyuka igazi.

Gilbert Syndrome uvame kutholakala izakhamuzi Afrika, nakuba kuyinto evamile phakathi abantu bezinye izizwe. By the way, amadoda yilesi sifo imayelana izikhathi 10 kakhulu ukudlula abantu besifazane.

Gilbert Syndrome: ukuthi kuyini futhi sibangelwa yini?

Lena isifo ngofuzo okuyinto lihlotshaniswa umsebenzi zezakhi zofuzo ezithile. Ngenxa yalokho, i-hepatocytes isibindi runningaway glucuronyl enganele. Kuyinto lokhu enzyme obangela yokubopha bilirubin ukuze glucuronic acid. Ngakho, nokushoda ketshezi asebenzayo kuholela aphakeme khulula sombala ophuzi egazini.

Gilbert Syndrome: kuyini futhi yiziphi izimpawu zaso?

Uphawu oyinhloko lesi sifo i-jaundice. Kufanele kuqashelwe ukuthi eziya ziba zimbi lesi sifo kungaba senziwa izici ezahlukene. Ikakhulukazi, ukuwohloka kwesimo sabantu siyenzeka ngenxa ukucindezeleka okunzima, ukukhathala ngokomzimba, ukungondleki noma indlala, ukusetshenziswa kwemithi ethile, kanye odlule esivimba amanzi isifo ukuvuvukala.

Mayelana nokwanda emakamu mahhala bilirubin egazini livela yellowness kwesikhumba futhi sclera. With ukuthuthukiswa nezinye izimpawu zesifo kungenzeka. Ezinye iziguli esekhala ikhanda, lokuhlushwa ukungakhuli, ukudideka, isiyezi, inkumbulo ukungakhuli. Ngezinye izikhathi kukhona umuzwa wokukhathazeka nokwesaba esilawulayo phansi ukuhlaselwa ukwethuka, futhi ngezinye izikhathi ukucindezeleka nokuqwasha.

Ngokwemvelo, kukhona iziyaluyalu wokugaya ukudla - is the ukungakuthandi ukudla, ukucanuzela kwenhliziyo, ubuhlungu besisu, amajaqamba endaweni kwesinye inyongo isibindi ngesisa, ukuvuvukala nohudo. Kwezinye izimo, ezikhulayo ukungabekezelelani ukudla okuthile, ezifana carbohydrate.

In the ukungabikho usizo ngesikhathi esifanele ukuze sibonakalise izimpawu ukwehluleka inhliziyo noma zokuphefumula, ukundindizela, ukoma ngokweqile, ukuhlanza ophikelelayo, ubuhlungu bemisipha, evuvukele zamanzi. Emacaleni angu-olunzima yokwehluleka kwesibindi acute eba.

Gilbert Syndrome: Ukwelashwa

Ngeshwa, ikhambi izifo zofuzo okwamanje akunakwenzeka. Ngakolunye uhlangothi, iningi isifo ingozi - eningi abantu amashumi eminyaka ngisho nokuwabona yokugula kwakhe. kokungenela Medical liyadingeka kuphela ngezikhathi exacerbation. Ngakho-ke, ngaleso kuqala izimpawu jaundice kufanele kudokotela. Umbhede ukuphumula, ukuphuza uketshezi oluningi, amavithamini kanye nokudla okufanele ukusiza kulesetayelekile umzimba. Kwezinye izimo, isiguli ezinqunyiwe phenobarbital, okuyinto kunciphisa lizinga bilirubin (ukusetshenziswa kwezidakamizwa bengayi ezinqumela, kusukela umthamo ayilungile kuze yezinkinga kungenzeka yokwehluleka kwesibindi). Ukudla akumele ifake imikhiqizo equkethe nezivimbelakuvunda kanye notshwala - ukudla kufanele kube fresh futhi mhlawumbe steamed.