I anomaly Arnold Chiari Uhlobo 1 - kuyini? Izimpawu, imiphumela, ukwelashwa

Akusiyo imfihlo ukuthi ngesikhathi kumiswa umbungu esibelethweni sikamama ngokujovwa abe zokugula ahlukahlukene kuhlanganise anomaly Arnold Chiari uhlobo 1. Kuyini lokhu sifo? Odokotela ukubiza lesi simanga ukungamukeleki esakheka ku-fetus ngenxa ukungafani usayizi kogebhezi ubuchopho, kwaku kuwo. Sikhuluma endaweni lapho cerebellum. Imiphumela iba yinhlanganisela yokukhandleka shift engxenyeni engenhla amalaka emgogodleni sihlukaniswe ngokuqukethwe sokwephulwa kwe olwengeziwe.

izimbangela

Ingabe abantu evamile khona, uma kutholwa anomaly Arnold Chiari uhlobo 1? Ubude bempilo, odokotela bathi, kuncike ezicini eziningana: degree kanye uhlobo lesi sifo. Ngaphambi wafaka le uphethwe wokugcina, zinikeza izimbangela ezaholela ukuthuthukiswa ukwahluka:

1. Azalwa naso. Okuningi e utero fetus skull ukusonteka kwenzeka: fossa Itholakala cerebellum, sincane kakhulu ngenxa yokukhula nokuthuthukisa grey ndaba. Phakathi kwezinye izizathu azalwa naso ekhonjiwe eqinile ukwanda foramen kombungu ngesikhathi kumiswa skeleton.
2. Uthenge i. Eyokuqala wathola ukulimala ekhanda ngesikhathi sokuzalwa. Futhi kulesi sigaba yilezi Ukulimala umgogodla: nomthelela ongemuhle oludakayo yakhe - uketshezi ekhethekile, okuvela kuyo iphimbo kanye nezinye umgogodla intambo kwezinso.

Zingagwegwesi kakhulu, efana ncamashí izizathu ososayensi abakwazi kodwa ukubiza. Okuwukuphela kwento uqiniseka ukuthi lesi sifo ongakaphathelani chromosomal kwezinso.

engcupheni

Wonke umuntu uyazi ukuthi phakathi nenkonzo senyanga yokuqala sokukhulelwa, i-fetus uya kuthebhu cishe zonke izinhlaka. Ngakho-ke, indlela efanele kokuphila kukanina ibaluleke kakhulu ukuthuthukiswa evamile ingane. Uma owesifazane alihambisani imithetho eyisisekelo esikhathini esizayo lokhu kubangela eziningi izinkinga. Kepha Chiari syndrome, ingozi ivela khona luyanda lezi zinto ezilandelayo:

• Bad imikhuba unina: ukubhema, ukusetshenziswa kabi kotshwala nezidakamizwa.
• Ukusetshenziswa kwezidakamizwa ezinamandla, zokuzelapha.
• Kudluliselwe izifo ezibangelwa amagciwane, ikakhulu nesimungumungwana.

Ngezinye amafomu ukukhanya kakhulu lesi sifo umntwana ozalwa engazizwa kuze kube sekupheleni kokuphila izimpawu ezikhethekile, ikakhulukazi uma sitholakale anomaly Arnold Chiari uhlobo 1. Bangakhi bantfwana bahlala, abanelungelo lwesithathu noma esigabeni sesine zesifo? Odokotela ukunikeza izibikezelo esidumazayo. Ngeshwa, ezifana ezimweni eziningi, izingane ezimiselwe ukufa. Ngisho noma ingane kutholakala lokuqala noma uhlobo isifo yesibili, kudingeka ukwelashwa: ukuhlinzwa, nekusebenta kuyinto 85%.

syndrome izinhlobo

Kungakhathaliseki namandla aso, konke ephathelene ne-isikhundla esiphansi kakhulu cerebellum. I ejulile amygdala phansi emseleni umgogodla, isifo esiyingozi kakhulu futhi akuqinisekile: naye ukuxilonga kanye nezinye kwezinso. Kususelwa kule nokunikeza 4 izinhlobo zokugula:

1. I anomaly Arnold Chiari Uhlobo 1 - yini lolu hlobo sifo? Ngokuvamile akubangi izinkinga enganeni. izinguquko ezihlelekile ebuchosheni ingekho, amalaka zitholakala kule ndawo wesibeletho.
2. yesibili uhlobo syndrome. Cerebellum kancane sigudluke ku Magnum foramen, ngesikhathi esifanayo kukhona umbungu ahlukahlukene kwezinso emgogodleni, asebuchosheni nomgogodla.
3. Lesi sifo uhlobo lwesithathu. Isakhiwo se-obungemuva is ngokuphelele elivulela Magnum foramen. kwakhiwa hernia is kule zoni.
4. Arnold Chiari sifo Uhlobo lwesine. It libhekene hypoplasia cerebellar - nokungathuthuki yayo. Nokho, lokhu akusho ukuthi ukunyakaza futhi ngokuvamile uhlanganiswa iphimbo kanye izinhlumba azalwa naso we posterior fossa cranial.

Odokotela bathi ukwenqaba uhlobo 2nd, 3rd futhi 4th ngokuvamile uxilongwe lihambisana namanye ukhubazeke kakhulu ekuthuthukiseni ingane: heterotopia we- cortex cerebral, subcortical izakhiwo hypoplasia, kwezinso we callosum Corpus , nokunye.

Izimpawu main

Njengoba sekushiwo, uma nesigaba lesi sifo ulula kakhulu, nobuchopho iyathinteka kancane, lesi sifo kungavuka cishe konke ukuphila kwakhe, ngaphandle kokuphazamisa umuntu. Kodwa lokhu kungase kwenzeke into eyivelakancane. Ngokuvamile bekhanda unomphela futhi njalo - uphawu eyinhloko lesi sifo anomaly Arnold Chiari uhlobo 1. Izimpawu yaleli fomu migraine ngaphandle kwalezi: ubuhlungu entanyeni, tinnitus, isicanucanu nokuhlanza, ubuthakathaka yezandla, nozwela ukulahlekelwa kwamalungu omzimba, ngisho phambi kwamehlo futhi umbono double, Gait engaqinisekile, inkulumo egwinya, futhi ecinene.

Ngokuphathelene syndrome yohlobo yesibili, okuyinto iyingozi kakhulu futhi kuyinkimbinkimbi, izimpawu zayo isici avele ngokushesha ngemva kokuzalwa noma zisencane kakhulu (ngokuvamile in zasenkulisa). Ngokuvamile kwesifuba kuyinto ukuphefumula ezinomsindo ezinsaneni, ukukhala ababuthakathaka, ukuphefumula nokugwinya. izinsana ezinjalo ngokushesha bavuselela futhi uzama ukulondoloza ngokusebenzisa ukuhlinzwa. Kulezi zimo, into esemqoka - ungaphuthelwa isikhashana lapho usengakwazi ukulondoloza ukuphila komntwana.

nezinye izimpawu

Basuke ebonwe degrees kakhulu yalesi sifo. imithombo eyinhloko ubuchopho esivimba amanzi noma umgogodla ngokuvamile izibonakaliso anomalies Arnold Chiari 1 hlobo akuyona ngakho kepha wesabeka njengezimpi nezinye zenyathi yakhe. Basuke izimpawu hhayi umbono kuphela kabili, kodwa ubumpumputhe ephelele, nokulahlekelwa ukwazi, ukulahlekelwa ukubambisana, ukuzamazama of emikhawulweni, izinkinga ne ukuchama, ukuba buthakathaka kwezicubu, ukulahlekelwa ukuzwa engxenyeni enkulu yomzimba (ngezinye izikhathi nesentimitha lonke zomzimba).

Kutfutfukiswa imiphumela ezahlukene zempilo kungabangela anomaly Arnold Chiari uhlobo 1. Ubude bempilo kanye nenkambo yayo evamile incike uphethwe esheshayo futhi enembile. Indlela kuphela ukuthola zokugula kuyinto MRI (magnetic resonance imaging) zobuchopho. Kudinga isimo lesiguli baxhashazwe ephelele, izingane ngakho okusebenzayo euthanized ngemithi ekhethekile. Ngosizo kule divayisi nazo liphenya yomgogodla, umgogodla, skeleton wesibeletho thoracic. MRI kungathola hhayi kuphela ngalesi sifo, kodwa zonke pathologies ezihambisana nalesi sifo.

yezinkinga

Kutfutfukiswa pathologies ezehlukene avuse anomaly Arnold Chiari uhlobo 1. Imiphumela zingase zishintshe kakhulu: kusuka arachnoiditis ezingamahlalakhona ziphethe izilonda parenchymal we Axon. Ikakhulukazi ngokukhazimulayo lezi yezinkinga zenzeka ngokumelene isizinda iziyaluyalu kwegazi emzimbeni emsipheni. iziyaluyalu Neuropsychiatric, kulesi simo avele kamuva futhi lwahlolwa ngesimo ukubambezeleka ukuthuthukiswa paraplegia. Uma anomaly ethuthuka kancane kancane kakhulu, kuholela iphimbo - ekuqongeleleni ngokweqile uketshezi ohlelweni ventricular zobuchopho.

Ngaphezu kwalokho, u-Arnold Chiari syndrome kungabangela kokucindezelwa enjalo enamandla emgogodleni lowo muntu ikhubazeke ngokuphelele. Ngaphansi umthelela walo omubi ngokuvamile ziqala ukwakheka izinhlumba kanye izimbotshana yomgogodla: abazitholayo ketshezi ephula umgogodla umsebenzi intambo. Libuye yezinkinga zingenzeka ukuphefumula lize lithi khimilili. Ngezinye izikhathi odokotela eqoshiwe iziguli inyumoniya congestive - iba umphumela yokuthi umuntu ulahlekelwa ikghono ngokukhululekile.

ukwelashwa ngoludala

Lesi sifo iphathwa ngu izindlela ezimbili. Odokotela akhethiwe indlela olandelanayo noma kuhlinzwa kuncike izimpawu zesifo esiboniswe nesineke, kobukhulu isimo somuntu, yezinkinga nemiphumela lesi sifo. Ngezinye izikhathi kuphela ukudla izidakamizwa kungabangela ukulwa nezifo ezifana Arnold Chiari uhlobo 1 anomaly. Hlobo luni yokwelapha? Okokuqala, udokotela iyaqhubeka nokwenza ukuhlolwa isimiso esiguli, oyiqondisayo ukuba umxhumanisi Ochwepheshe ezahlukene, ubani emva kokuxoxisana uzathatha izinyathelo ezifanele.

Uma isiguli ekhononda zobuhlungu esifundeni occipital lwekhanda noma entanyeni, wagunyaza amaphilisi ezinhlungu namanxusa eqeda ukuvuvukala, kanye imithi ezisiza ukukhulula imisipha. Kuyasiza kakhulu futhi okhethekile umsebenzi zokwelapha - uzivivinye okuhloswe ngalo ukuqeda ethuthumela ezingalweni nasemilenzeni, kanye ukuzinza kokuxhumana. Ngenxa yalezi zinjongo, njengoba kushiwo yokwelapha esebenzayo emsebenzini. Nokuningi kuyoba amaseshini ewusizo nodokotela osiza abanezinkinga zokukhuluma, ngubani uzokwazi ukususa nenkinga ngenkulumo. Konke lokhu izindlela kungaba noma zivimbele ngokuphelele ekufezeni yokwelashwa nolaka - ukuhlinzwa.

kokungenela kuhlinzwa

Kwenzeka ukuthi izinyathelo ezingenhla ukusiza - ngenkuthalo uyaqhubeka ukuthuthukisa futhi abakhulule kweqembu kokuhlupheka Arnold Chiari uhlobo 1 anomaly. Ukwelashwa abese eshintsha kakhulu: udokotela iqala ukulungiselela umuntu ukuhlinzwa. ukusebenza Neurosurgical siqhutshwa Okuqondiwe ezintathu. Okokuqala, ukuqeda izimpawu ezibalulekile ezinjengalezi izifo, ezifana nokulahlekelwa ukwazi, ukuphazamiseka visual, ukuba buthakathaka kwezicubu. Okwesibili, kokungenela kusiza ukususa umthombo oyinhloko izimpawu - ukuqeda kokucindezelwa zobuchopho. Okwesithathu, usebenzisa yi operation in izinga ukunyakazisa oludakayo.

Ukungenela Kumiswe inqubo yezinguquko isakhiwo yomgogodla kanye grey ndaba: ngenxa izimpawu abohle, isiguli eseqala ukuzwa kangcono. Ngokuvamile, odokotela abahlinzayo kusukela ezingemuva isuswe fossa cranial ithambo isinqamu: isikhala kwandisa ubuchopho, grey ndaba iyeke ukuba dengwane kanye isibambo. Futhi incipha intracranial ingcindezi. Ngaphezu kwalokho, odokotela ngenkuthalo ngekusebentisa emasu lafana ngokuxhunyelelwa kanye nokuvala umsele umgogodla.

zokuvimbela

Ukuthi ingane azange abe nezinkinga ngenhla, umama okhulelwe kufanele zingathathi izinto kalula mayelana isikhundla sabo. Okokuqala, kumelwe ubuyekeze yonke kwezinso kungenzeka ukuthi kungenzeka i-fetus: kombungu neural tube, Down Syndrome, u-Arnold Chiari uhlobo 1 anomaly. Siyini ngempela lesi sifo, kungani zenzeka, futhi iziphi izinyathelo zingafundwa ukunciphisa ingozi lezi nezinye kwezinso, kufanele wazi zonke umama okhulelwe. owesifazane okhulelwe abanekhono futhi uyazi sizokwazi ukugwema zonke izici ukuthi abe nomthelela omubi kumiswa umbungu.

Okwesibili, owesifazane ubophekile ukuba adle ngokugcwele, udle ezihlukahlukene ukudla okunempilo: inhlanzi, inyama, izithelo, imifino, okusanhlamvu kanye nemikhiqizo yobisi. It akuvunyelwe akuvumelekile utshwala. Futhi, udinga ukuyeka ukubhema, ingasaphathwa izidakamizwa izidakamizwa ezinamandla. Noma yimuphi umuthi, ngisho homeopathic, umama okhulelwe uthatha kuphela ngemva somuthi nokusetshenziswa kwawo sikadokotela. Okwesithathu, owesifazane naye unomsebenzi omningi ukuhamba, ukuphefumula umoya ohlanzekile, ukuhambisa eziningi. Mayelana imizwa, imizwelo kanye nemizwelo emibi kuyinto ukukhohlwa, ejabulela isikhundla sakhe futhi uthole injabulo okungcono kakhulu ekuphileni.