ImpiloIzifo nemibandela

Hemolytic-uremic syndrome - kuyini?

Hemolytic uremic syndrome kuyinto uphawu, okuyinto kubonakala ngesimo anaemia hemolytic, OPN futhi thrombocytopenia. Ngokokuqala ngqá lesi sifo wayechazwa ngo-1955. Ngokusho kochwepheshe, mayelana 70% amacala uphethwe ezinganeni konyaka wokuqala wokuphila, futhi kuphela ezigigabeni ezimbalwa ezilotshwe abadala. Kulesi sihloko sizoxoxa ngalesi sifo, futhi sibheke indlela selashwe yezindlela zesimanje hemolytic uremic syndrome.

izimbangela ezisheshayo

Ukuthuthukiswa kwale Ochwepheshe isifo ngaleso namuhla lihlotshaniswa ezicini eziningana. Ngokuyinhloko lokhu viral ngqo anobuthi umonakalo capillary endothelium kangaka okuthiwa glomeruli. Ngakolunye uhlangothi isizathu angase aqambe amanga ku DIC futhi umonakalo mechanical kuya erythrocyte. Kukholakala ukuthi lona wamuva kungalimala ngesikhathi nokuwela capillary ye glomeruli ngokwabo, okuyizinto ithuba egcwele fibrin amahlule.

izimpawu eziyinhloko

Hemolytic-uremic syndrome kwenzeka ogxile nezingane ukwehla ngokushesha umchamo okukhipha, kodwa ngenxa yokuntuleka kwezinhlelo ezibanzi izimpawu ezisobala amanzi emzimbeni futhi isizinda veo imingcele okuvamile. Uma ingane has a imfiva noma ukuhlanza uvele okungenzeka kakhulu isifo siqhubeka ngokushesha - kwakukhona edema palsy. Ngokuvamile, hemolytic uremic syndrome is kwahambisana by ingane okhanyayo kubantu abanebala elikhanyayo, ezimweni ezingavamile, ne nokuqhuma ezincane.

ekuxilongweni

Ukuze lokhu ngoba uyayazi imbangela ezifana hemolytic-uremic syndrome, Uzodlula kokuxilongwa, kuhlanganise ephelele igazi ukuhlaziywa. Kuphela ngemuva luhlolo egcwele isiguli ukhulume okunye ukwelashwa.

izindlela zesimanje ukwelashwa

Muva nje inikezwe uphethwe ngokwempilo yangenyama laliphezulu kakhulu (80 kuya ku-100%). Nokho, ososayensi njalo ufuna ikhambi lale nkinga. Ngakho-ke sidalwe amadivayisi ngokuthi "izinso yokufakelwa", sibonga ngalo isimo sesishintshile kakhulu. Namuhla, nokufa cishe ziphinde zenzeke (phakathi ezimbili futhi eziyishumi amaphesenti). Kungenzeka kuphela ngesikhathi ngasekupheleni isifo ukuthola, kanye nokuthuthukiswa izinqubo engelapheki ebuchosheni ngenxa ukuvuvukala yayo. Kufanele kuqashelwe ukuthi enjalo uphethwe atypical uremic hemolytic syndrome, ngokuvamile kudinga kusuka 2 kuya 9 izikhathi (nsuku zonke) usebenzisa "izinso yokufakelwa". Ngalokhu zelashwe Ochwepheshe singalondoloza amazinga evamile metabolites, kanye ukuvimbela ubuchopho ukuvuvukala.

ukuba nombono ongafani ngeke

izindlela zesimanje uvumele izingane ukuba sibhekane nale nkinga. Nokho, lokhu kungenzeka kuphela uma kwenzeka ukuthi ukugula itholiwe ngezigaba zayo zokuqala. Kungenjalo, amathuba ngokugcwele alulame ngandlela-thile aphansi. Ngokusho kochwepheshe, isimo ngokungabi bikho impendulo omuhle ingxenye yomzimba emva 2-3 izikhathi hemodialysis, izibikezelo ezingezinhle kakhulu.

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